Histologic and immunohistochemical features of the skin lesions in CANDLE syndrome

American Journal of Dermatopathology

Volumn 37, Issue 7, 2015, Pages 517-522

  Torrelo, Antonio ^a   Colmenero, Isabel ^b   Requena, Luis ^c   Paller, Amy S ^d   Ramot, Yuval ^e   Lee, Chyi Chia Richard ^f   Vera, Angel ^g   Zlotogorski, Abraham ^f   Goldbach Mansky, Raphaela ^h   Kutzner, Heinz ⁱ  

^a HOSPITAL INFANTIL UNIVERSITARIO NIÑO JESÚS   (Spain)

^b BIRMINGHAM CHILDREN S HOSPITAL   (United Kingdom)

^c Hospital UniversitarioFundación Jiménez Díaz   (Spain)

^d NORTHWESTERN UNIVERSITY   (United States)

^e HADASSAH HEBREW UNIVERSITY MEDICAL CENTER   (Israel)

^f NATIONAL CANCER INSTITUTE   (United States)

^g HOSPITAL REGIONAL UNIVERSITARIO DE MÁLAGA   (Spain)

^h NATIONAL INSTITUTE OF ARTHRITIS AND MUSCULOSKELETAL AND SKIN DISEASES   (United States)

ⁱ Dermatopathologische Gemeinschaftspraxis   (Germany)

Author keywords

Autoinflammation; CANDLE syndrome; Histopathology; Immunohistochemistry; Interferons; PSMB8

Indexed keywords

CD123 ANTIGEN; CD14 ANTIGEN; CD163 ANTIGEN; CD33 ANTIGEN; CD68 ANTIGEN; MYELOPEROXIDASE; PMG1 PROTEIN; PROTEIN; UNCLASSIFIED DRUG; CD68 ANTIGEN, HUMAN; CELL SURFACE RECEPTOR; DIFFERENTIATION ANTIGEN; IL3RA PROTEIN, HUMAN; LEUKOCYTE ANTIGEN; PEROXIDASE;

ARTICLE; BONE MARROW CELL; CHRONIC ATYPICAL NEUTROPHILIC DERMATOSIS WITH LIPODYSTROPHY AND ELEVATED TEMPERATURE SYNDROME; CLINICAL ARTICLE; EOSINOPHIL; HISTIOCYTE; HISTOLOGY; HISTOPATHOLOGY; HUMAN; HUMAN TISSUE; IMMUNOHISTOCHEMISTRY; INFLAMMATORY INFILTRATE; LIPODYSTROPHY; LYMPHOCYTE; MACROPHAGE; MONONUCLEAR CELL; NEUTROPHIL; PATHOGENESIS; PLASMACYTOID DENDRITIC CELL; PRIORITY JOURNAL; REGULATORY T LYMPHOCYTE; SKIN BIOPSY; SKIN DISEASE; CHEMISTRY; CHRONIC DISEASE; DENDRITIC CELL; FEVER; METABOLISM; PATHOLOGY; SYNDROME;

ANTIGENS, CD; ANTIGENS, DIFFERENTIATION, MYELOMONOCYTIC; CHRONIC DISEASE; DENDRITIC CELLS; EOSINOPHILS; FEVER; HISTIOCYTES; HUMANS; IMMUNOHISTOCHEMISTRY; INTERLEUKIN-3 RECEPTOR ALPHA SUBUNIT; LIPODYSTROPHY; LYMPHOCYTES; MACROPHAGES; MYELOID CELLS; NEUTROPHILS; PEROXIDASE; RECEPTORS, CELL SURFACE; SKIN DISEASES; SYNDROME;

EID: 84942565152     PISSN: 01931091     EISSN: 15330311     Source Type: Journal    
DOI: 10.1097/DAD.0000000000000340     Document Type: Article

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