Modeling and study of the mechanism of dilated cardiomyopathy using induced pluripotent stem cells derived from individuals with duchenne muscular dystrophy

DMM Disease Models and Mechanisms

Volumn 8, Issue 5, 2015, Pages 457-466

  Lin, Bo ^a   Li, Yang ^a   Han, Lu ^a   Kaplan, Aaron D ^b   Ao, Ying ^a   Kalra, Spandan ^c   Bett, Glenna C L ^b   Rasmusson, Randall L ^b   Denning, Chris ^c   Yang, Lei ^a  

^a UNIVERSITY OF PITTSBURGH SCHOOL OF MEDICINE   (United States)

^b UNIVERSITY AT BUFFALO   (United States)

^c UNIVERSITY OF NOTTINGHAM   (United Kingdom)

Author keywords

Dilated cardiomyopathy; Duchenne muscular dystrophy; Induced pluripotent stem cells

Indexed keywords

CASPASE 3; DYSTROPHIN; POLOXAMER; CALCIUM; TRANSCRIPTOME;

APOPTOSIS; ARTICLE; CELL DEATH; CELL DIFFERENTIATION; CONGESTIVE CARDIOMYOPATHY; CONTROLLED STUDY; DISEASE COURSE; DUCHENNE MUSCULAR DYSTROPHY; ENZYME ACTIVATION; GENE MUTATION; HEART MUSCLE CELL; HUMAN; HUMAN CELL; IN VITRO STUDY; MEMBRANE POTENTIAL; MITOCHONDRION; MUSCLE WEAKNESS; MUSCULAR DYSTROPHY; PHENOTYPE; PLURIPOTENT STEM CELL; PRIORITY JOURNAL; TRANSMISSION ELECTRON MICROSCOPY; WESTERN BLOTTING; ADOLESCENT; ANIMAL; CARDIAC MUSCLE CELL; CARDIOMYOPATHY, DILATED; CYTOLOGY; DISEASE MODEL; DRUG EFFECTS; GENETICS; INDUCED PLURIPOTENT STEM CELL; MALE; METABOLISM; MOUSE; MUSCULAR DYSTROPHY, ANIMAL; MUSCULAR DYSTROPHY, DUCHENNE; PATHOLOGY; SEQUENCE ANALYSIS; SIGNAL TRANSDUCTION; ULTRASTRUCTURE;

ADOLESCENT; ANIMALS; APOPTOSIS; CALCIUM; CARDIOMYOPATHY, DILATED; CASPASE 3; CELL DIFFERENTIATION; DISEASE MODELS, ANIMAL; HUMANS; INDUCED PLURIPOTENT STEM CELLS; MALE; MICE; MITOCHONDRIA; MUSCULAR DYSTROPHY, ANIMAL; MUSCULAR DYSTROPHY, DUCHENNE; MYOCYTES, CARDIAC; POLOXAMER; SEQUENCE ANALYSIS, RNA; SIGNAL TRANSDUCTION; TRANSCRIPTOME;

EID: 84928994904     PISSN: 17548403     EISSN: 17548411     Source Type: Journal    
DOI: 10.1242/dmm.019505     Document Type: Article

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