The effects of bisphosphonates on ectopic soft tissue mineralization caused by mutations in the abcc6 gene

Cell Cycle

Volumn 14, Issue 7, 2015, Pages 1082-1089

  Li, Qiaoli ^a   Sundberg, John P ^b   Levine, Michael A ^c   Terry, Sharon F ^d   Uitto, Jouni ^a  

^a THOMAS JEFFERSON UNIVERSITY   (United States)

^b JACKSON LABORATORY   (United States)

^c CHILDREN S HOSPITAL OF PHILADELPHIA   (United States)

^d PXE International   (United States)

Author keywords

Bisphosphonates; Ectopic mineralization; Generalized arterial calcification of infancy; Pseudoxanthoma elasticum

Indexed keywords

ALENDRONIC ACID; BIOLOGICAL MARKER; BISPHOSPHONIC ACID DERIVATIVE; CALCIUM; ETIDRONIC ACID; MINERAL; MULTIDRUG RESISTANCE ASSOCIATED PROTEIN 6; PHOSPHORUS; ABC TRANSPORTER; ABCC6 PROTEIN, MOUSE; BONE DENSITY CONSERVATION AGENT;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTERY CALCIFICATION; ARTICLE; BONE MINERALIZATION; COMPUTED TOMOGRAPHY SCANNER; CONTROLLED STUDY; DIET; DRUG EFFECT; FEMALE; FEMUR; GENE MUTATION; GENERALIZED ARTERIAL CALCIFICATION OF INFANCY; GENETIC DISORDER; HISTOPATHOLOGY; KNOCKOUT MOUSE; MALE; MICRO-COMPUTED TOMOGRAPHY; MINERALIZATION; MORPHOLOGY; MOUSE; NONHUMAN; PSEUDOXANTHOMA ELASTICUM; QUANTITATIVE ANALYSIS; SOFT TISSUE CALCIFICATION; TRABECULAR BONE; VIBRISSA; ANIMAL; C57BL MOUSE; DRUG EFFECTS; GENETICS; HUMAN; MUTATION; PATHOLOGY; PRECLINICAL STUDY; SKIN; VASCULAR CALCIFICATION;

MUS;

ALENDRONATE; ANIMALS; ATP-BINDING CASSETTE TRANSPORTERS; BONE DENSITY CONSERVATION AGENTS; DRUG EVALUATION, PRECLINICAL; ETIDRONIC ACID; FEMALE; FEMUR; HUMANS; MALE; MICE, INBRED C57BL; MICE, KNOCKOUT; MUTATION; PSEUDOXANTHOMA ELASTICUM; SKIN; VASCULAR CALCIFICATION;

EID: 84928102584     PISSN: 15384101     EISSN: 15514005     Source Type: Journal    
DOI: 10.1080/15384101.2015.1007809     Document Type: Article

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