Urea cycle disorders: A case report of a successful treatment with liver transplant and a literature review

World Journal of Gastroenterology

Volumn 21, Issue 13, 2015, Pages 4063-4068

  Foschi, Francesco Giuseppe ^a   Morelli, Maria Cristina ^b   Savini, Sara ^a   Dall'Aglio, Anna Chiara ^a   Lanzi, Arianna ^a   Cescon, Matteo ^b   Ercolani, Giorgio ^b   Cucchetti, Alessandro ^b   Pinna, Antonio Daniele ^b   Stefanini, Giuseppe Francesco ^a  

^a Ospedale di Faenza   (Italy)

^b UNIVERSITY OF BOLOGNA   (Italy)

Author keywords

Diet; Hyperammonemia; Liver transplantation; Quality of life; Urea cycle disorders

Indexed keywords

AMMONIA; ARGININE; BENZOIC ACID; CARBAMATE KINASE; IMMUNOSUPPRESSIVE AGENT;

ADOLESCENT; AMMONIA BLOOD LEVEL; ARTICLE; ATAXIA; CASE REPORT; COGNITIVE DEFECT; COORDINATION DISORDER; DIET RESTRICTION; FEMALE; GROWTH RETARDATION; HUMAN; HYPERAMMONEMIA; IMMUNOSUPPRESSIVE TREATMENT; LETHARGY; LIVER GRAFT REJECTION; LIVER TRANSPLANTATION; SOMNOLENCE; UREA CYCLE DISORDER; CARBAMOYL-PHOSPHATE SYNTHASE I DEFICIENCY DISEASE; COMPLICATION; DIET THERAPY; DISEASE COURSE; PROTEIN RESTRICTION; QUALITY OF LIFE; TREATMENT OUTCOME;

ADOLESCENT; CARBAMOYL-PHOSPHATE SYNTHASE I DEFICIENCY DISEASE; DIET, PROTEIN-RESTRICTED; DISEASE PROGRESSION; FEMALE; HUMANS; HYPERAMMONEMIA; LIVER TRANSPLANTATION; QUALITY OF LIFE; TREATMENT OUTCOME;

EID: 84926630202     PISSN: 10079327     EISSN: 22192840     Source Type: Journal    
DOI: 10.3748/wjg.v21.i13.4063     Document Type: Article

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