High urgency liver transplantation in ornithine transcarbamylase deficiency presenting with acute liver failure

Pediatric Transplantation

Volumn 15, Issue 6, 2011, Pages

  Teufel, Ulrike ^a   Weitz, Jürgen ^a   Flechtenmacher, Christa ^a   Prietsch, Viola ^b   Schmidt, Jan ^a   Hoffmann, Georg F ^a   Kölker, Stefan ^a   Engelmann, Guido ^a  

^a UNIVERSITY OF HEIDELBERG   (Germany)

^b STÄDTISCHES KLINIKUM KARLSRUHE   (Germany)

Author keywords

acute liver failure; metabolic; pediatric liver transplantation; urea cycle disorder

Indexed keywords

4 PHENYLBUTYRIC ACID; ARGININE; BASILIXIMAB; BENZOIC ACID; BLOOD CLOTTING FACTOR; CYCLOSPORIN A; FRESH FROZEN PLASMA; METHYLPREDNISOLONE; PREDNISOLONE; VITAMIN K GROUP;

ACUTE LIVER FAILURE; ARTICLE; BLOOD TRANSFUSION; CASE REPORT; CHILD; CLINICAL FEATURE; COMA; DIFFERENTIAL DIAGNOSIS; FEMALE; HEPATIC ENCEPHALOPATHY; HERPES VIRUS INFECTION; HUMAN; IMMUNOSUPPRESSIVE TREATMENT; LIVER GRAFT REJECTION; LIVER TRANSPLANTATION; MUTATIONAL ANALYSIS; ORNITHINE TRANSCARBAMYLASE DEFICIENCY; PRESCHOOL CHILD; PROTEIN RESTRICTION; UREA CYCLE;

ALANINE TRANSAMINASE; ASPARTATE AMINOTRANSFERASES; CHILD, PRESCHOOL; FEMALE; HEPATIC ENCEPHALOPATHY; HUMANS; LIVER FAILURE, ACUTE; LIVER TRANSPLANTATION; ORNITHINE CARBAMOYLTRANSFERASE DEFICIENCY DISEASE; PREVALENCE; TREATMENT OUTCOME; UREA;

EID: 80052095884     PISSN: 13973142     EISSN: 13993046     Source Type: Journal    
DOI: 10.1111/j.1399-3046.2009.01171.x     Document Type: Article

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