Liver transplantation for non-hepatotoxic inborn errors of metabolism

Current Gastroenterology Reports

Volumn 8, Issue 3, 2006, Pages 215-223

  Treem, William R ^a  

^a SUNY DOWNSTATE MEDICAL CENTER   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

AMINO ACID; ARGININOSUCCINATE SYNTHASE; BLOOD CLOTTING FACTOR 7; CARBAMOYL PHOSPHATE SYNTHASE; CARNITINE; CITRIC ACID; FRESH FROZEN PLASMA; MAGNESIUM; METRONIDAZOLE; ORNITHINE CARBAMOYLTRANSFERASE; OXALIC ACID; PHOSPHATE; PROTEIN C; PYRIDOXINE; RECOMBINANT BLOOD CLOTTING FACTOR 7A; STARCH; WARFARIN;

AUTISM; BLOOD CLOTTING FACTOR 7 DEFICIENCY; BLOOD TRANSFUSION; CARDIOMYOPATHY; CHILD CARE; CITRULLINEMIA; CRIGLER NAJJAR SYNDROME; DIET RESTRICTION; DISEASE CONTROL; ENZYME DEFICIENCY; ENZYME REPLACEMENT; EXTRAPYRAMIDAL SYMPTOM; FAMILIAL HYPERCHOLESTEROLEMIA; GLYCOGEN STORAGE DISEASE; HEMODIALYSIS; HEPATOCYTE TRANSPLANTATION; HETEROZYGOTE; HUMAN; INBORN ERROR OF METABOLISM; LIVER CELL; LIVER DISEASE; LIVER FAILURE; LIVER TRANSPLANTATION; LIVING DONOR; MENTAL DISEASE; METHYLMALONIC ACIDEMIA; MYOPATHY; NITROGEN METABOLISM; OPTIC NERVE ATROPHY; OXALOSIS 1; PANCREATITIS; PERCEPTION DEAFNESS; PHOTOTHERAPY; PROPIONIC ACIDEMIA; PROTEIN C DEFICIENCY; REVIEW; TREATMENT INDICATION; UREA CYCLE;

CHILD; DISEASE PROGRESSION; HUMANS; LIVER DISEASES; LIVER TRANSPLANTATION; METABOLISM, INBORN ERRORS; TIME FACTORS; TREATMENT OUTCOME;

EID: 33744971594     PISSN: 15228037     EISSN: None     Source Type: Journal    
DOI: 10.1007/s11894-006-0078-5     Document Type: Review

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