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Volumn 36, Issue 2, 2015, Pages 169-179

Primary ciliary dyskinesia

Author keywords

bronchiectasis; cilia; ciliary dyskinesia; dynein arms; otitis; Pseudomonas aeruginosa; sinusitis; situs inversus

Indexed keywords

ANTIBIOTIC AGENT; ANTIINFLAMMATORY AGENT; DEOXYRIBONUCLEASE; NITRIC OXIDE; OSMOTIC AGENT; SACCHARIN; ANTIINFECTIVE AGENT;

EID: 84926141467     PISSN: 10693424     EISSN: 10989048     Source Type: Journal    
DOI: 10.1055/s-0035-1546748     Document Type: Article
Times cited : (48)

References (71)
  • 1
    • 0442313529 scopus 로고    scopus 로고
    • Primary ciliary dyskinesia: Diagnostic and phenotypic features
    • Noone P. G., Leigh M. W., Sannuti A., et al. Primary ciliary dyskinesia: diagnostic and phenotypic features. Am J Respir Crit Care Med: 2004; 169 4 459 467
    • (2004) Am J Respir Crit Care Med , vol.169 , Issue.4 , pp. 459-467
    • Noone, P.G.1    Leigh, M.W.2    Sannuti, A.3
  • 2
    • 0017162819 scopus 로고
    • A human syndrome caused by immotile cilia
    • Afzelius B. A. A human syndrome caused by immotile cilia. Science: 1976; 193 4250 317 319
    • (1976) Science , vol.193 , Issue.4250 , pp. 317-319
    • Afzelius, B.A.1
  • 3
    • 0017744878 scopus 로고
    • The immotile-cilia syndrome. A congenital ciliary abnormality as an etiologic factor in chronic airway infections and male sterility
    • Eliasson R., Mossberg B., Camner P., Afzelius B. A. The immotile-cilia syndrome. A congenital ciliary abnormality as an etiologic factor in chronic airway infections and male sterility. N Engl J Med: 1977; 297 1 1 6
    • (1977) N Engl J Med , vol.297 , Issue.1 , pp. 1-6
    • Eliasson, R.1    Mossberg, B.2    Camner, P.3    Afzelius, B.A.4
  • 4
    • 0018341965 scopus 로고
    • Cilia with defective radial spokes: A cause of human respiratory disease
    • Sturgess J. M., Chao J., Wong J., Aspin N., Turner J. A. Cilia with defective radial spokes: a cause of human respiratory disease. N Engl J Med: 1979; 300 2 53 56
    • (1979) N Engl J Med , vol.300 , Issue.2 , pp. 53-56
    • Sturgess, J.M.1    Chao, J.2    Wong, J.3    Aspin, N.4    Turner, J.A.5
  • 5
    • 0018831497 scopus 로고
    • Abnormal cilia in Polynesians with bronchiectasis
    • Wakefield S., Waite D. Abnormal cilia in Polynesians with bronchiectasis. Am Rev Respir Dis: 1980; 121 6 1003 1010
    • (1980) Am Rev Respir Dis , vol.121 , Issue.6 , pp. 1003-1010
    • Wakefield, S.1    Waite, D.2
  • 6
    • 0009731921 scopus 로고
    • Normal ciliary ultrastructure in children with Kartagener's syndrome
    • Herzon F. S., Murphy S. Normal ciliary ultrastructure in children with Kartagener's syndrome. Ann Otol Rhinol Laryngol: 1980; 89 1, Pt 1 81 83
    • (1980) Ann Otol Rhinol Laryngol , vol.89 , Issue.1 , pp. 81-83
    • Herzon, F.S.1    Murphy, S.2
  • 7
    • 80053035330 scopus 로고    scopus 로고
    • The challenges of diagnosing primary ciliary dyskinesia
    • Leigh M. W., O'Callaghan C., Knowles M. R. The challenges of diagnosing primary ciliary dyskinesia. Proc Am Thorac Soc: 2011; 8 5 434 437
    • (2011) Proc Am Thorac Soc , vol.8 , Issue.5 , pp. 434-437
    • Leigh, M.W.1    O'Callaghan, C.2    Knowles, M.R.3
  • 9
    • 0037385839 scopus 로고    scopus 로고
    • Functional analysis of cilia and ciliated epithelial ultrastructure in healthy children and young adults
    • Chilvers M. A., Rutman A., O'Callaghan C. Functional analysis of cilia and ciliated epithelial ultrastructure in healthy children and young adults. Thorax: 2003; 58 4 333 338
    • (2003) Thorax , vol.58 , Issue.4 , pp. 333-338
    • Chilvers, M.A.1    Rutman, A.2    O'Callaghan, C.3
  • 10
    • 33947384151 scopus 로고    scopus 로고
    • Overview of structure and function of mammalian cilia
    • Satir P., Christensen S. T. Overview of structure and function of mammalian cilia. Annu Rev Physiol: 2007; 69 377 400
    • (2007) Annu Rev Physiol , vol.69 , pp. 377-400
    • Satir, P.1    Christensen, S.T.2
  • 11
    • 33947525850 scopus 로고    scopus 로고
    • Genetic defects in ciliary structure and function
    • Zariwala M. A., Knowles M. R., Omran H. Genetic defects in ciliary structure and function. Annu Rev Physiol: 2007; 69 423 450
    • (2007) Annu Rev Physiol , vol.69 , pp. 423-450
    • Zariwala, M.A.1    Knowles, M.R.2    Omran, H.3
  • 12
    • 67349154436 scopus 로고    scopus 로고
    • The PCP pathway instructs the planar orientation of ciliated cells in the Xenopus larval skin
    • Mitchell B., Stubbs J. L., Huisman F., Taborek P., Yu C., Kintner C. The PCP pathway instructs the planar orientation of ciliated cells in the Xenopus larval skin. Curr Biol: 2009; 19 11 924 929
    • (2009) Curr Biol , vol.19 , Issue.11 , pp. 924-929
    • Mitchell, B.1    Stubbs, J.L.2    Huisman, F.3    Taborek, P.4    Yu, C.5    Kintner, C.6
  • 13
    • 34247555530 scopus 로고    scopus 로고
    • A positive feedback mechanism governs the polarity and motion of motile cilia
    • Mitchell B., Jacobs R., Li J., Chien S., Kintner C. A positive feedback mechanism governs the polarity and motion of motile cilia. Nature: 2007; 447 7140 97 101
    • (2007) Nature , vol.447 , Issue.7140 , pp. 97-101
    • Mitchell, B.1    Jacobs, R.2    Li, J.3    Chien, S.4    Kintner, C.5
  • 15
    • 58149345576 scopus 로고    scopus 로고
    • Cilia multifunctional organelles at the center of vertebrate left-right asymmetry
    • Basu B., Brueckner M. Cilia multifunctional organelles at the center of vertebrate left-right asymmetry. Curr Top Dev Biol: 2008; 85 151 174
    • (2008) Curr Top Dev Biol , vol.85 , pp. 151-174
    • Basu, B.1    Brueckner, M.2
  • 16
    • 80053001262 scopus 로고    scopus 로고
    • Update of respiratory tract disease in children with primary ciliary dyskinesia
    • Sagel S. D., Davis S. D., Campisi P., Dell S. D. Update of respiratory tract disease in children with primary ciliary dyskinesia. Proc Am Thorac Soc: 2011; 8 5 438 443
    • (2011) Proc Am Thorac Soc , vol.8 , Issue.5 , pp. 438-443
    • Sagel, S.D.1    Davis, S.D.2    Campisi, P.3    Dell, S.D.4
  • 17
    • 34249661222 scopus 로고    scopus 로고
    • Primary ciliary dyskinesia and newborn respiratory distress
    • Ferkol T., Leigh M. Primary ciliary dyskinesia and newborn respiratory distress. Semin Perinatol: 2006; 30 6 335 340
    • (2006) Semin Perinatol , vol.30 , Issue.6 , pp. 335-340
    • Ferkol, T.1    Leigh, M.2
  • 18
    • 43249128903 scopus 로고    scopus 로고
    • Early lung disease in young children with primary ciliary dyskinesia
    • Brown D. E., Pittman J. E., Leigh M. W., Fordham L., Davis S. D. Early lung disease in young children with primary ciliary dyskinesia. Pediatr Pulmonol: 2008; 43 5 514 516
    • (2008) Pediatr Pulmonol , vol.43 , Issue.5 , pp. 514-516
    • Brown, D.E.1    Pittman, J.E.2    Leigh, M.W.3    Fordham, L.4    Davis, S.D.5
  • 19
    • 49449118909 scopus 로고    scopus 로고
    • Structural and functional lung disease in primary ciliary dyskinesia
    • Santamaria F., Montella S., Tiddens H. A., et al. Structural and functional lung disease in primary ciliary dyskinesia. Chest: 2008; 134 2 351 357
    • (2008) Chest , vol.134 , Issue.2 , pp. 351-357
    • Santamaria, F.1    Montella, S.2    Tiddens, H.A.3
  • 21
    • 34247571813 scopus 로고    scopus 로고
    • High-resolution CT of patients with primary ciliary dyskinesia
    • Kennedy M. P., Noone P. G., Leigh M. W., et al. High-resolution CT of patients with primary ciliary dyskinesia. AJR Am J Roentgenol: 2007; 188 5 1232 1238
    • (2007) AJR Am J Roentgenol , vol.188 , Issue.5 , pp. 1232-1238
    • Kennedy, M.P.1    Noone, P.G.2    Leigh, M.W.3
  • 22
    • 34548268622 scopus 로고    scopus 로고
    • Primary ciliary dyskinesia in the paediatric population: Range and severity of radiological findings in a cohort of patients receiving tertiary care
    • Jain K., Padley S. P., Goldstraw E. J., et al. Primary ciliary dyskinesia in the paediatric population: range and severity of radiological findings in a cohort of patients receiving tertiary care. Clin Radiol: 2007; 62 10 986 993
    • (2007) Clin Radiol , vol.62 , Issue.10 , pp. 986-993
    • Jain, K.1    Padley, S.P.2    Goldstraw, E.J.3
  • 23
    • 34247598971 scopus 로고    scopus 로고
    • Congenital heart disease and other heterotaxic defects in a large cohort of patients with primary ciliary dyskinesia
    • Kennedy M. P., Omran H., Leigh M. W., et al. Congenital heart disease and other heterotaxic defects in a large cohort of patients with primary ciliary dyskinesia. Circulation: 2007; 115 22 2814 2821
    • (2007) Circulation , vol.115 , Issue.22 , pp. 2814-2821
    • Kennedy, M.P.1    Omran, H.2    Leigh, M.W.3
  • 24
    • 0028246542 scopus 로고
    • Fertility in men with primary ciliary dyskinesia presenting with respiratory infection
    • Munro N. C., Currie D. C., Lindsay K. S., et al. Fertility in men with primary ciliary dyskinesia presenting with respiratory infection. Thorax: 1994; 49 7 684 687
    • (1994) Thorax , vol.49 , Issue.7 , pp. 684-687
    • Munro, N.C.1    Currie, D.C.2    Lindsay, K.S.3
  • 25
    • 0027637074 scopus 로고
    • New associations of primary ciliary dyskinesia syndrome
    • Engesaeth V. G., Warner J. O., Bush A. New associations of primary ciliary dyskinesia syndrome. Pediatr Pulmonol: 1993; 16 1 9 12
    • (1993) Pediatr Pulmonol , vol.16 , Issue.1 , pp. 9-12
    • Engesaeth, V.G.1    Warner, J.O.2    Bush, A.3
  • 27
    • 73249125649 scopus 로고    scopus 로고
    • Primary ciliary dyskinesia: A consensus statement on diagnostic and treatment approaches in children
    • Barbato A., Frischer T., Kuehni C. E., et al. Primary ciliary dyskinesia: a consensus statement on diagnostic and treatment approaches in children. Eur Respir J: 2009; 34 6 1264 1276
    • (2009) Eur Respir J , vol.34 , Issue.6 , pp. 1264-1276
    • Barbato, A.1    Frischer, T.2    Kuehni, C.E.3
  • 29
    • 84886431107 scopus 로고    scopus 로고
    • Standardizing nasal nitric oxide measurement as a test for primary ciliary dyskinesia
    • Leigh M. W., Hazucha M. J., Chawla K. K., et al. Standardizing nasal nitric oxide measurement as a test for primary ciliary dyskinesia. Ann Am Thorac Soc: 2013; 10 6 574 581
    • (2013) Ann Am Thorac Soc , vol.10 , Issue.6 , pp. 574-581
    • Leigh, M.W.1    Hazucha, M.J.2    Chawla, K.K.3
  • 31
    • 79960203777 scopus 로고    scopus 로고
    • Primary ciliary dyskinesia: Evaluation using cilia beat frequency assessment via spectral analysis of digital microscopy images
    • Olm M. A., Kögler J. E. Jr, Macchione M., Shoemark A., Saldiva P. H., Rodrigues J. C. Primary ciliary dyskinesia: evaluation using cilia beat frequency assessment via spectral analysis of digital microscopy images. J Appl Physiol (1985): 2011; 111 1 295 302
    • (2011) J Appl Physiol (1985) , vol.111 , Issue.1 , pp. 295-302
    • Olm, M.A.1    Kögler, J.E.2    Macchione, M.3    Shoemark, A.4    Saldiva, P.H.5    Rodrigues, J.C.6
  • 34
    • 84857360976 scopus 로고    scopus 로고
    • Twenty-year review of quantitative transmission electron microscopy for the diagnosis of primary ciliary dyskinesia
    • Shoemark A., Dixon M., Corrin B., Dewar A. Twenty-year review of quantitative transmission electron microscopy for the diagnosis of primary ciliary dyskinesia. J Clin Pathol: 2012; 65 3 267 271
    • (2012) J Clin Pathol , vol.65 , Issue.3 , pp. 267-271
    • Shoemark, A.1    Dixon, M.2    Corrin, B.3    Dewar, A.4
  • 35
    • 0042235314 scopus 로고    scopus 로고
    • Ciliary beat pattern is associated with specific ultrastructural defects in primary ciliary dyskinesia
    • Chilvers M. A., Rutman A., O'Callaghan C. Ciliary beat pattern is associated with specific ultrastructural defects in primary ciliary dyskinesia. J Allergy Clin Immunol: 2003; 112 3 518 524
    • (2003) J Allergy Clin Immunol , vol.112 , Issue.3 , pp. 518-524
    • Chilvers, M.A.1    Rutman, A.2    O'Callaghan, C.3
  • 36
    • 80053061098 scopus 로고    scopus 로고
    • Inner dynein arm defects causing primary ciliary dyskinesia: Repeat testing required
    • O'Callaghan C., Rutman A., Williams G. M., Hirst R. A. Inner dynein arm defects causing primary ciliary dyskinesia: repeat testing required. Eur Respir J: 2011; 38 3 603 607
    • (2011) Eur Respir J , vol.38 , Issue.3 , pp. 603-607
    • O'Callaghan, C.1    Rutman, A.2    Williams, G.M.3    Hirst, R.A.4
  • 37
    • 2942756190 scopus 로고    scopus 로고
    • The secondary nature of ciliary (dis)orientation in secondary and primary ciliary dyskinesia
    • Jorissen M., Willems T. The secondary nature of ciliary (dis)orientation in secondary and primary ciliary dyskinesia. Acta Otolaryngol: 2004; 124 4 527 531
    • (2004) Acta Otolaryngol , vol.124 , Issue.4 , pp. 527-531
    • Jorissen, M.1    Willems, T.2
  • 38
    • 79954992693 scopus 로고    scopus 로고
    • Diagnostic yield of nasal scrape biopsies in primary ciliary dyskinesia: A multicenter experience
    • Genetic Disorders of Mucociliary Clearance Consortium
    • Olin J. T., Burns K., Carson J. L., et al. Genetic Disorders of Mucociliary Clearance Consortium. Diagnostic yield of nasal scrape biopsies in primary ciliary dyskinesia: a multicenter experience. Pediatr Pulmonol: 2011; 46 5 483 488
    • (2011) Pediatr Pulmonol , vol.46 , Issue.5 , pp. 483-488
    • Olin, J.T.1    Burns, K.2    Carson, J.L.3
  • 39
    • 34249676831 scopus 로고    scopus 로고
    • Genetic causes of bronchiectasis: Primary ciliary dyskinesia
    • Morillas H. N., Zariwala M., Knowles M. R. Genetic causes of bronchiectasis: primary ciliary dyskinesia. Respiration: 2007; 74 3 252 263
    • (2007) Respiration , vol.74 , Issue.3 , pp. 252-263
    • Morillas, H.N.1    Zariwala, M.2    Knowles, M.R.3
  • 40
    • 84861640948 scopus 로고    scopus 로고
    • CCDC103 mutations cause primary ciliary dyskinesia by disrupting assembly of ciliary dynein arms
    • Panizzi J. R., Becker-Heck A., Castleman V. H., et al. CCDC103 mutations cause primary ciliary dyskinesia by disrupting assembly of ciliary dynein arms. Nat Genet: 2012; 44 6 714 719
    • (2012) Nat Genet , vol.44 , Issue.6 , pp. 714-719
    • Panizzi, J.R.1    Becker-Heck, A.2    Castleman, V.H.3
  • 42
    • 78651260210 scopus 로고    scopus 로고
    • CCDC39 is required for assembly of inner dynein arms and the dynein regulatory complex and for normal ciliary motility in humans and dogs
    • Merveille A. C., Davis E. E., Becker-Heck A., et al. CCDC39 is required for assembly of inner dynein arms and the dynein regulatory complex and for normal ciliary motility in humans and dogs. Nat Genet: 2011; 43 1 72 78
    • (2011) Nat Genet , vol.43 , Issue.1 , pp. 72-78
    • Merveille, A.C.1    Davis, E.E.2    Becker-Heck, A.3
  • 43
    • 84873988112 scopus 로고    scopus 로고
    • Mutations in CCDC39 and CCDC40 are the major cause of primary ciliary dyskinesia with axonemal disorganization and absent inner dynein arms
    • Uk10k
    • Antony D., Becker-Heck A., Zariwala M. A., et al. Uk10k. Mutations in CCDC39 and CCDC40 are the major cause of primary ciliary dyskinesia with axonemal disorganization and absent inner dynein arms. Hum Mutat: 2013; 34 3 462 472
    • (2013) Hum Mutat , vol.34 , Issue.3 , pp. 462-472
    • Antony, D.1    Becker-Heck, A.2    Zariwala, M.A.3
  • 44
    • 84867244938 scopus 로고    scopus 로고
    • Recessive HYDIN mutations cause primary ciliary dyskinesia without randomization of left-right body asymmetry
    • UK10K Consortium
    • Olbrich H., Schmidts M., Werner C., et al. UK10K Consortium. Recessive HYDIN mutations cause primary ciliary dyskinesia without randomization of left-right body asymmetry. Am J Hum Genet: 2012; 91 4 672 684
    • (2012) Am J Hum Genet , vol.91 , Issue.4 , pp. 672-684
    • Olbrich, H.1    Schmidts, M.2    Werner, C.3
  • 45
    • 33646120587 scopus 로고    scopus 로고
    • Axonemal localization of the dynein component DNAH5 is not altered in secondary ciliary dyskinesia
    • Olbrich H., Horváth J., Fekete A., et al. Axonemal localization of the dynein component DNAH5 is not altered in secondary ciliary dyskinesia. Pediatr Res: 2006; 59 3 418 422
    • (2006) Pediatr Res , vol.59 , Issue.3 , pp. 418-422
    • Olbrich, H.1    Horváth, J.2    Fekete, A.3
  • 46
    • 84867259922 scopus 로고    scopus 로고
    • Whole-exome capture and sequencing identifies HEATR2 mutation as a cause of primary ciliary dyskinesia
    • Horani A., Druley T. E., Zariwala M. A., et al. Whole-exome capture and sequencing identifies HEATR2 mutation as a cause of primary ciliary dyskinesia. Am J Hum Genet: 2012; 91 4 685 693
    • (2012) Am J Hum Genet , vol.91 , Issue.4 , pp. 685-693
    • Horani, A.1    Druley, T.E.2    Zariwala, M.A.3
  • 47
    • 84868384681 scopus 로고    scopus 로고
    • Loss-of-function mutations in LRRC6, a gene essential for proper axonemal assembly of inner and outer dynein arms, cause primary ciliary dyskinesia
    • Kott E., Duquesnoy P., Copin B., et al. Loss-of-function mutations in LRRC6, a gene essential for proper axonemal assembly of inner and outer dynein arms, cause primary ciliary dyskinesia. Am J Hum Genet: 2012; 91 5 958 964
    • (2012) Am J Hum Genet , vol.91 , Issue.5 , pp. 958-964
    • Kott, E.1    Duquesnoy, P.2    Copin, B.3
  • 48
    • 79955856801 scopus 로고    scopus 로고
    • Primary ciliary dyskinesia caused by homozygous mutation in DNAL1, encoding dynein light chain 1
    • Mazor M., Alkrinawi S., Chalifa-Caspi V., et al. Primary ciliary dyskinesia caused by homozygous mutation in DNAL1, encoding dynein light chain 1. Am J Hum Genet: 2011; 88 5 599 607
    • (2011) Am J Hum Genet , vol.88 , Issue.5 , pp. 599-607
    • Mazor, M.1    Alkrinawi, S.2    Chalifa-Caspi, V.3
  • 49
    • 84906274398 scopus 로고    scopus 로고
    • MCIDAS mutations result in a mucociliary clearance disorder with reduced generation of multiple motile cilia
    • Boon M., Wallmeier J., Ma L., et al. MCIDAS mutations result in a mucociliary clearance disorder with reduced generation of multiple motile cilia. Nat Commun: 2014; 5 4418
    • (2014) Nat Commun , vol.5 , pp. 4418
    • Boon, M.1    Wallmeier, J.2    Ma, L.3
  • 50
    • 84896137851 scopus 로고    scopus 로고
    • Robust diagnostic genetic testing using solution capture enrichment and a novel variant-filtering interface
    • Watson C. M., Crinnion L. A., Morgan J. E., et al. Robust diagnostic genetic testing using solution capture enrichment and a novel variant-filtering interface. Hum Mutat: 2014; 35 4 434 441
    • (2014) Hum Mutat , vol.35 , Issue.4 , pp. 434-441
    • Watson, C.M.1    Crinnion, L.A.2    Morgan, J.E.3
  • 51
    • 0032811712 scopus 로고    scopus 로고
    • Effect of aerosolized uridine-5′-triphosphate on airway clearance with cough in patients with primary ciliary dyskinesia
    • Noone P. G., Bennett W. D., Regnis J. A., et al. Effect of aerosolized uridine-5′-triphosphate on airway clearance with cough in patients with primary ciliary dyskinesia. Am J Respir Crit Care Med: 1999; 160 1 144 149
    • (1999) Am J Respir Crit Care Med , vol.160 , Issue.1 , pp. 144-149
    • Noone, P.G.1    Bennett, W.D.2    Regnis, J.A.3
  • 52
    • 81155137837 scopus 로고    scopus 로고
    • Nebulised 7% hypertonic saline improves lung function and quality of life in bronchiectasis
    • Kellett F., Robert N. M. Nebulised 7% hypertonic saline improves lung function and quality of life in bronchiectasis. Respir Med: 2011; 105 12 1831 1835
    • (2011) Respir Med , vol.105 , Issue.12 , pp. 1831-1835
    • Kellett, F.1    Robert, N.M.2
  • 53
    • 84919692674 scopus 로고    scopus 로고
    • Inhaled mannitol for non-cystic fibrosis bronchiectasis: A randomised, controlled trial
    • B-305 Study Investigators
    • Bilton D., Tino G., Barker A. F., et al. B-305 Study Investigators. Inhaled mannitol for non-cystic fibrosis bronchiectasis: a randomised, controlled trial. Thorax: 2014; 69 12 1073 1079
    • (2014) Thorax , vol.69 , Issue.12 , pp. 1073-1079
    • Bilton, D.1    Tino, G.2    Barker, A.F.3
  • 54
    • 0028129568 scopus 로고
    • Effect of aerosolized recombinant human DNase on exacerbations of respiratory symptoms and on pulmonary function in patients with cystic fibrosis
    • The Pulmozyme Study Group
    • Fuchs H. J., Borowitz D. S., Christiansen D. H., et al. The Pulmozyme Study Group. Effect of aerosolized recombinant human DNase on exacerbations of respiratory symptoms and on pulmonary function in patients with cystic fibrosis. N Engl J Med: 1994; 331 10 637 642
    • (1994) N Engl J Med , vol.331 , Issue.10 , pp. 637-642
    • Fuchs, H.J.1    Borowitz, D.S.2    Christiansen, D.H.3
  • 55
    • 0031901989 scopus 로고    scopus 로고
    • Treatment of idiopathic bronchiectasis with aerosolized recombinant human DNase I. RhDNase Study Group
    • O'Donnell A. E., Barker A. F., Ilowite J. S., Fick R. B. Treatment of idiopathic bronchiectasis with aerosolized recombinant human DNase I. rhDNase Study Group. Chest: 1998; 113 5 1329 1334
    • (1998) Chest , vol.113 , Issue.5 , pp. 1329-1334
    • O'Donnell, A.E.1    Barker, A.F.2    Ilowite, J.S.3    Fick, R.B.4
  • 56
    • 36248953255 scopus 로고    scopus 로고
    • Cystic fibrosis pulmonary guidelines: Chronic medications for maintenance of lung health
    • Cystic Fibrosis Foundation, Pulmonary Therapies Committee
    • Flume P. A., O'Sullivan B. P., Robinson K. A., et al. Cystic Fibrosis Foundation, Pulmonary Therapies Committee. Cystic fibrosis pulmonary guidelines: chronic medications for maintenance of lung health. Am J Respir Crit Care Med: 2007; 176 10 957 969
    • (2007) Am J Respir Crit Care Med , vol.176 , Issue.10 , pp. 957-969
    • Flume, P.A.1    O'Sullivan, B.P.2    Robinson, K.A.3
  • 57
    • 84857422474 scopus 로고    scopus 로고
    • Use of antibiotics in bronchiectasis
    • King P. T., Holmes P. W. Use of antibiotics in bronchiectasis. Rev Recent Clin Trials: 2012; 7 1 24 30
    • (2012) Rev Recent Clin Trials , vol.7 , Issue.1 , pp. 24-30
    • King, P.T.1    Holmes, P.W.2
  • 58
    • 79951824943 scopus 로고    scopus 로고
    • A randomized controlled trial of nebulized gentamicin in non-cystic fibrosis bronchiectasis
    • Murray M. P., Govan J. R., Doherty C. J., et al. A randomized controlled trial of nebulized gentamicin in non-cystic fibrosis bronchiectasis. Am J Respir Crit Care Med: 2011; 183 4 491 499
    • (2011) Am J Respir Crit Care Med , vol.183 , Issue.4 , pp. 491-499
    • Murray, M.P.1    Govan, J.R.2    Doherty, C.J.3
  • 59
    • 84908070796 scopus 로고    scopus 로고
    • Aztreonam for inhalation solution in patients with non-cystic fibrosis bronchiectasis (AIR-BX1 and AIR-BX2): Two randomised double-blind, placebo-controlled phase 3 trials
    • Barker A. F., O'Donnell A. E., Flume P., et al. Aztreonam for inhalation solution in patients with non-cystic fibrosis bronchiectasis (AIR-BX1 and AIR-BX2): two randomised double-blind, placebo-controlled phase 3 trials. Lancet Respir Med: 2014; 2 9 738 749
    • (2014) Lancet Respir Med , vol.2 , Issue.9 , pp. 738-749
    • Barker, A.F.1    O'Donnell, A.E.2    Flume, P.3
  • 60
    • 84898994995 scopus 로고    scopus 로고
    • Inhaled colistin in patients with bronchiectasis and chronic Pseudomonas aeruginosa infection
    • Haworth C. S., Foweraker J. E., Wilkinson P., Kenyon R. F., Bilton D. Inhaled colistin in patients with bronchiectasis and chronic Pseudomonas aeruginosa infection. Am J Respir Crit Care Med: 2014; 189 8 975 982
    • (2014) Am J Respir Crit Care Med , vol.189 , Issue.8 , pp. 975-982
    • Haworth, C.S.1    Foweraker, J.E.2    Wilkinson, P.3    Kenyon, R.F.4    Bilton, D.5
  • 61
    • 41649101361 scopus 로고    scopus 로고
    • Prolonged antibiotics for purulent bronchiectasis in children and adults
    • Evans D. J., Bara A. I., Greenstone M. Prolonged antibiotics for purulent bronchiectasis in children and adults. Cochrane Database Syst Rev: 2007; 2 CD001392
    • (2007) Cochrane Database Syst Rev , Issue.2 , pp. CD001392
    • Evans, D.J.1    Bara, A.I.2    Greenstone, M.3
  • 62
    • 84855887761 scopus 로고    scopus 로고
    • Outcomes of Pseudomonas eradication therapy in patients with non-cystic fibrosis bronchiectasis
    • White L., Mirrani G., Grover M., Rollason J., Malin A., Suntharalingam J. Outcomes of Pseudomonas eradication therapy in patients with non-cystic fibrosis bronchiectasis. Respir Med: 2012; 106 3 356 360
    • (2012) Respir Med , vol.106 , Issue.3 , pp. 356-360
    • White, L.1    Mirrani, G.2    Grover, M.3    Rollason, J.4    Malin, A.5    Suntharalingam, J.6
  • 63
    • 84875543900 scopus 로고    scopus 로고
    • Effect of long-term, low-dose erythromycin on pulmonary exacerbations among patients with non-cystic fibrosis bronchiectasis: The BLESS randomized controlled trial
    • Serisier D. J., Martin M. L., McGuckin M. A., et al. Effect of long-term, low-dose erythromycin on pulmonary exacerbations among patients with non-cystic fibrosis bronchiectasis: the BLESS randomized controlled trial. JAMA: 2013; 309 12 1260 1267
    • (2013) JAMA , vol.309 , Issue.12 , pp. 1260-1267
    • Serisier, D.J.1    Martin, M.L.2    McGuckin, M.A.3
  • 64
    • 84875524849 scopus 로고    scopus 로고
    • Effect of azithromycin maintenance treatment on infectious exacerbations among patients with non-cystic fibrosis bronchiectasis: The BAT randomized controlled trial
    • Altenburg J., de Graaff C. S., Stienstra Y., et al. Effect of azithromycin maintenance treatment on infectious exacerbations among patients with non-cystic fibrosis bronchiectasis: the BAT randomized controlled trial. JAMA: 2013; 309 12 1251 1259
    • (2013) JAMA , vol.309 , Issue.12 , pp. 1251-1259
    • Altenburg, J.1    De Graaff, C.S.2    Stienstra, Y.3
  • 65
    • 84865131777 scopus 로고    scopus 로고
    • Azithromycin for prevention of exacerbations in non-cystic fibrosis bronchiectasis (EMBRACE): A randomised, double-blind, placebo-controlled trial
    • Wong C., Jayaram L., Karalus N., et al. Azithromycin for prevention of exacerbations in non-cystic fibrosis bronchiectasis (EMBRACE): a randomised, double-blind, placebo-controlled trial. Lancet: 2012; 380 9842 660 667
    • (2012) Lancet , vol.380 , Issue.9842 , pp. 660-667
    • Wong, C.1    Jayaram, L.2    Karalus, N.3
  • 66
    • 0030013750 scopus 로고    scopus 로고
    • Is resection of bronchiectasis beneficial in patients with primary ciliary dyskinesia
    • Smit H. J., Schreurs A. J., Van den Bosch J. M., Westermann C. J. Is resection of bronchiectasis beneficial in patients with primary ciliary dyskinesia? Chest: 1996; 109 6 1541 1544
    • (1996) Chest , vol.109 , Issue.6 , pp. 1541-1544
    • Smit, H.J.1    Schreurs, A.J.2    Van Den Bosch, J.M.3    Westermann, C.J.4
  • 67
    • 84866127151 scopus 로고    scopus 로고
    • The Registry of the International Society for Heart and Lung Transplantation: 29th adult lung and heart-lung transplant report-2012
    • International Society of Heart and Lung Transplantation
    • Christie J. D., Edwards L. B., Kucheryavaya A. Y., et al. International Society of Heart and Lung Transplantation. The Registry of the International Society for Heart and Lung Transplantation: 29th adult lung and heart-lung transplant report-2012. J Heart Lung Transplant: 2012; 31 10 1073 1086
    • (2012) J Heart Lung Transplant , vol.31 , Issue.10 , pp. 1073-1086
    • Christie, J.D.1    Edwards, L.B.2    Kucheryavaya, A.Y.3
  • 68
    • 84857062817 scopus 로고    scopus 로고
    • Managing upper respiratory tract complications of primary ciliary dyskinesia in children
    • Campbell R. Managing upper respiratory tract complications of primary ciliary dyskinesia in children. Curr Opin Allergy Clin Immunol: 2012; 12 1 32 38
    • (2012) Curr Opin Allergy Clin Immunol , vol.12 , Issue.1 , pp. 32-38
    • Campbell, R.1
  • 70
    • 0027360561 scopus 로고
    • A treatment for primary ciliary dyskinesia: Efficacy of functional endoscopic sinus surgery
    • (11, Pt 1)
    • Parsons D. S., Greene B. A. A treatment for primary ciliary dyskinesia: efficacy of functional endoscopic sinus surgery. Laryngoscope: 1993; 103 (11, Pt 1): 1269 1272
    • (1993) Laryngoscope , vol.103 , pp. 1269-1272
    • Parsons, D.S.1    Greene, B.A.2
  • 71
    • 0030698259 scopus 로고    scopus 로고
    • Longitudinal study of lung function in a cohort of primary ciliary dyskinesia
    • Ellerman A., Bisgaard H. Longitudinal study of lung function in a cohort of primary ciliary dyskinesia. Eur Respir J: 1997; 10 10 2376 2379
    • (1997) Eur Respir J , vol.10 , Issue.10 , pp. 2376-2379
    • Ellerman, A.1    Bisgaard, H.2


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