Primary ciliary dyskinesia: A consensus statement on diagnostic and treatment approaches in children

European Respiratory Journal

Volumn 34, Issue 6, 2009, Pages 1264-1276

  Barbato, A ^a   Frischer, T ^b   Kuehni, C E ^d   Snijders, D ^a   Azevedo, I ^f   Baktai, G ^g   Bartoloni, L ^e   Eber, E ^c   Escribano, A ^h   Haarman, E ⁱ   Hesselmar, B ^j   Hogg, C ^k   Jorissen, M ⁿ   Lucas, J ^l   Nielsen, K G ^o   O'Callaghan, C ^m   Omran, H ^p   Pohunek, P ^q   Strippoli, M P F ^d   Bush, A ^k  

^a UNIVERSITY OF PADOVA   (Italy)

^b UNIVERSITY OF VIENNA   (Austria)

^c MEDICAL UNIVERSITY OF GRAZ   (Austria)

^d UNIVERSITY OF BERN   (Switzerland)

^e UNIVERSITY OF GENEVA MEDICAL SCHOOL   (Switzerland)

^f HOSPITAL DE SÃO JOÃO   (Portugal)

^g Svabhegy Pediatric Institute   (Hungary)

^h HOSPITAL CLÍNICO UNIVERSITARIO   (Spain)

ⁱ EMMA CHILDREN S HOSPITAL   (Netherlands)

^j SAHLGRENSKA ACADEMY AT UNIVERSITY OF GOTHENBURG   (Sweden)

^k ROYAL BROMPTON HOSPITAL   (United Kingdom)

^l UNIVERSITY HOSPITAL SOUTHAMPTON NHS FOUNDATION TRUST   (United Kingdom)

^m UNIVERSITY OF LEICESTER   (United Kingdom)

ⁿ UNIVERSITY HOSPITALS LEUVEN   (Belgium)

^o Rigshospitalet   (Denmark)

^p UNIVERSITY OF FREIBURG   (Germany)

^q UNIVERSITY HOSPITAL MOTOL   (Czech Republic)

more..

Author keywords

Consensus statement; Diagnosis; Primary ciliary dyskinesia; Treatment

Indexed keywords

ANTIBIOTIC AGENT; CORTICOSTEROID DERIVATIVE; DORNASE ALFA; DYNEIN ADENOSINE TRIPHOSPHATASE; NITRIC OXIDE; PREDNISOLONE; SACCHARIN;

BRONCHIECTASIS; BRONCHOSCOPY; CILIARY DYSKINESIA; CILIARY MOTILITY; CILIATED EPITHELIUM; CONFERENCE PAPER; DRUG MEGADOSE; DYNEIN AXONEMAL HEAVY CHAIN 11 GENE; DYNEIN AXONEMAL HEAVY CHAIN 5 GENE; DYNEIN AXONEMAL INTERMEDIATE CHAIN 1 GENE; DYNEIN AXONEMAL INTERMEDIATE CHAIN 2 GENE; ELECTRON MICROSCOPY; ENVIRONMENTAL EXPOSURE; GENE; GENE MUTATION; GENETIC ANALYSIS; HUMAN; IMMUNIZATION; INHERITANCE; KTU GENE; LOBECTOMY; LUNG INFECTION; MEDICAL SOCIETY; MUCOCILIARY CLEARANCE; ORAL FACIAL DIGITAL SYNDROME 1 GENE; OTITIS MEDIA; PREVALENCE; PRIORITY JOURNAL; PROTEIN LOCALIZATION; RETINITIS PIGMENTOSA GUANOSINE TRIPHOSPHATASE REGULATOR GENE; RSPH4A GENE; RSPH9 GENE; SCREENING TEST; THORAX RADIOGRAPHY; TRANSMISSION ELECTRON MICROSCOPY; TXNDC3 GENE;

ADULT; CHILD; CLINICAL TRIALS AS TOPIC; FEMALE; HUMANS; KARTAGENER SYNDROME; MALE; MICROSCOPY, ELECTRON, TRANSMISSION; PHENOTYPE; PULMONARY MEDICINE; RESPIRATORY SYSTEM; SPERM MOTILITY; TREATMENT OUTCOME;

EID: 73249125649     PISSN: 09031936     EISSN: 13993003     Source Type: Journal    
DOI: 10.1183/09031936.00176608     Document Type: Conference Paper

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