Mechanisms of plasma non-transferrin bound iron generation: Insights from comparing transfused diamond blackfan anaemia with sickle cell and thalassaemia patients

British Journal of Haematology

Volumn 167, Issue 5, 2014, Pages 692-696

  Porter, John B ^a   Walter, Patrick B ^b,c   Neumayr, Lynne D ^b   Evans, Patricia ^a   Bansal, Sukhvinder ^d   Garbowski, Maciej ^a   Weyhmiller, Marcela G ^b   Harmatz, Paul R ^b   Wood, John C ^e   Miller, Jeffery L ^f   Byrnes, Colleen ^f   Weiss, Guenter ^g   Seifert, Markus ^g   Grosse, Regine ^h   Grabowski, Dagmar ^h   Schmidt, Angelica ^h   Fischer, Roland ^h   Nielsen, Peter ^h   Niemeyer, Charlotte ⁱ   Vichinsky, Elliott ^b  

^a UNIVERSITY COLLEGE LONDON   (United Kingdom)

^b CHILDREN S HOSPITAL OAKLAND   (United States)

^c UNIVERSITY OF VICTORIA   (Canada)

^d KING'S COLLEGE LONDON   (United Kingdom)

^e CHILDREN S HOSPITAL LOS ANGELES   (United States)

^f NATIONAL INSTITUTE OF DIABETES AND DIGESTIVE AND KIDNEY DISEASES   (United States)

^g INNSBRUCK MEDICAL UNIVERSITY   (Austria)

^h UNIVERSITY MEDICAL CENTER HAMBURG EPPENDORF   (Germany)

ⁱ UNIVERSITY OF FREIBURG   (Germany)

Author keywords

Erythropoiesis; Hepcidin; Inflammation; Iron overload; Non transferrin bound iron; NTBI

Indexed keywords

ERYTHROPOIETIN; FERROPORTIN; GROWTH DIFFERENTIATION FACTOR 15; IRON DERIVATIVE; LABILE PLASMA IRON; NON TRANSFERRIN BOUND IRON; TRANSFERRIN; TRANSFERRIN RECEPTOR; UNCLASSIFIED DRUG; BIOLOGICAL MARKER; IRON; PLASMA PROTEIN;

ADOLESCENT; ADULT; ARTICLE; BLACKFAN DIAMOND ANEMIA; BLOOD SAMPLING; BLOOD TRANSFUSION; CHELATION THERAPY; CHILD; CLINICAL ARTICLE; CONTROLLED STUDY; ERYTHROPOIESIS; FERRITIN BLOOD LEVEL; HUMAN; HYPOXEMIA; IRON BLOOD LEVEL; IRON METABOLISM; IRON OVERLOAD; LIVER LEVEL; PRIORITY JOURNAL; SICKLE CELL ANEMIA; THALASSEMIA MAJOR; ANEMIA, DIAMOND-BLACKFAN; ANEMIA, SICKLE CELL; BLOOD; CLINICAL TRIAL; COMPARATIVE STUDY; FEMALE; MALE; METABOLISM; MULTICENTER STUDY; THALASSEMIA;

ADOLESCENT; ADULT; ANEMIA, DIAMOND-BLACKFAN; ANEMIA, SICKLE CELL; BIOLOGICAL MARKERS; BLOOD PROTEINS; BLOOD TRANSFUSION; ERYTHROPOIESIS; FEMALE; HUMANS; IRON; IRON OVERLOAD; MALE; THALASSEMIA; TRANSFERRIN;

EID: 84925224042     PISSN: 00071048     EISSN: 13652141     Source Type: Journal    
DOI: 10.1111/bjh.13081     Document Type: Article

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