-
1
-
-
84879350647
-
Atypical hemolytic uremic syndrome: What is it, how is it diagnosed, and how is it treated?
-
Nester CM, Thomas CP: Atypical hemolytic uremic syndrome: what is it, how is it diagnosed, and how is it treated? Hematology Am Soc Hematol Educ Program, 2012; 2012: 617–25.
-
(2012)
Hematology am Soc Hematol Educ Program
, vol.2012
, pp. 617-625
-
-
Nester, C.M.1
Thomas, C.P.2
-
2
-
-
0037158606
-
Thrombotic microangiopathies
-
Moake JL: Thrombotic microangiopathies. N Engl J Med, 2002; 347(8): 589–600.
-
(2002)
N Engl J Med
, vol.347
, Issue.8
, pp. 589-600
-
-
Moake, J.L.1
-
3
-
-
2542490269
-
Effect of plasma exchange on plasma ADAMTS13 metalloprotease activity, inhibitor level, and clinical outcome in patients with idiopathic and nonidiopathic thrombotic thrombocytopenic purpura
-
Zheng XL1, Kaufman RM, Goodnough LT, Sadler JE: Effect of plasma exchange on plasma ADAMTS13 metalloprotease activity, inhibitor level, and clinical outcome in patients with idiopathic and nonidiopathic thrombotic thrombocytopenic purpura. Blood, 2004; 103(11): 4043–9.
-
(2004)
Blood
, vol.103
, Issue.11
, pp. 4043-4049
-
-
Xl1, Z.1
Kaufman, R.M.2
Goodnough, L.T.3
Sadler, J.E.4
-
4
-
-
77949903692
-
Survival and relapse in patients with thrombotic thrombocytopenic purpura
-
quiz 1662
-
Kremer Hovinga JA, Vesely SK, Terrell DR et al: Survival and relapse in patients with thrombotic thrombocytopenic purpura. Blood, 2010; 115 (8): 1500–11; quiz 1662.
-
(2010)
Blood
, vol.115
, Issue.8
, pp. 1500-1511
-
-
Kremer Hovinga, J.A.1
Vesely, S.K.2
Terrell, D.R.3
-
5
-
-
34547633064
-
Differential impact of complement mutations on clinical characteristics in atypical hemolytic uremic syndrome
-
Sellier-Leclerc AL, Fremeaux-Bacchi V, Dragon-Durey MA et al: Differential impact of complement mutations on clinical characteristics in atypical hemolytic uremic syndrome. J Am Soc Nephrol, 2007; 18(8): 2392–400.
-
(2007)
J am Soc Nephrol
, vol.18
, Issue.8
, pp. 2392-2400
-
-
Sellier-Leclerc, A.L.1
Fremeaux-Bacchi, V.2
Dragon-Durey, M.A.3
-
6
-
-
0029823536
-
Typical and atypical hemolytic uremic syndrome
-
Proesmans, W: Typical and atypical hemolytic uremic syndrome. Kidney Blood Press Res, 1996; 19(3–4): 205–8.
-
(1996)
Kidney Blood Press Res
, vol.19
, Issue.34
, pp. 205-208
-
-
Proesmans, W.1
-
7
-
-
70350279315
-
Atypical hemolytic-uremic syndrome
-
Noris M, Remuzzi G: Atypical hemolytic-uremic syndrome. N Engl J Med, 2009; 361(17): 1676–87.
-
(2009)
N Engl J Med
, vol.361
, Issue.17
, pp. 1676-1687
-
-
Noris, M.1
Remuzzi, G.2
-
8
-
-
84883557853
-
Atypical hemolytic uremic syndrome and thrombotic thrombocytopenic purpura: Clinically differentiating the thrombotic microangiopathies
-
Cataland SR, Wu HM: Atypical hemolytic uremic syndrome and thrombotic thrombocytopenic purpura: clinically differentiating the thrombotic microangiopathies. Eur J Intern Med, 2013; 24(6): 486–91.
-
(2013)
Eur J Intern Med
, vol.24
, Issue.6
, pp. 486-491
-
-
Cataland, S.R.1
Wu, H.M.2
-
9
-
-
84896695246
-
Diagnostic criteria for atypical hemolytic uremic syndrome proposed by the Joint Committee of the Japanese Society of Nephrology and the Japan Pediatric Society
-
Sawai T, Nangaku M, Ashida A et al: Diagnostic criteria for atypical hemolytic uremic syndrome proposed by the Joint Committee of the Japanese Society of Nephrology and the Japan Pediatric Society. Clin Exp Nephrol, 2014; 18(1): 4–9.
-
(2014)
Clin Exp Nephrol
, vol.18
, Issue.1
, pp. 4-9
-
-
Sawai, T.1
Nangaku, M.2
Ashida, A.3
-
10
-
-
0031970553
-
Genetic studies into inherited and sporadic hemolytic uremic syndrome
-
Warwicker P, Goodship TH, Donne RL et al: Genetic studies into inherited and sporadic hemolytic uremic syndrome. Kidney Int, 1998; 53(4): 836–44.
-
(1998)
Kidney Int
, vol.53
, Issue.4
, pp. 836-844
-
-
Warwicker, P.1
Goodship, T.H.2
Donne, R.L.3
-
11
-
-
0035128326
-
Factor H mutations in hemolytic uremic syndrome cluster in exons 18–20, a domain important for host cell recognition
-
Richards A, Buddles MR, Donne RL et al: Factor H mutations in hemolytic uremic syndrome cluster in exons 18–20, a domain important for host cell recognition. Am J Hum Genet, 2001; 68(2): 485–90.
-
(2001)
Am J Hum Genet
, vol.68
, Issue.2
, pp. 485-490
-
-
Richards, A.1
Buddles, M.R.2
Donne, R.L.3
-
12
-
-
2342650263
-
Mutations in CD46, a complement regulatory protein, predispose to atypical HUS
-
Goodship TH, Liszewski MK, Kemp EJ et al: Mutations in CD46, a complement regulatory protein, predispose to atypical HUS. Trends Mol Med, 2004; 10(5): 226–31.
-
(2004)
Trends Mol Med
, vol.10
, Issue.5
, pp. 226-231
-
-
Goodship, T.H.1
Liszewski, M.K.2
Kemp, E.J.3
-
13
-
-
0242331610
-
Mutations in human complement regulator, membrane cofactor protein (CD46), predispose to development of familial hemolytic uremic syndrome
-
Richards A, Kemp EJ, Liszewski MK et al: Mutations in human complement regulator, membrane cofactor protein (CD46), predispose to development of familial hemolytic uremic syndrome. Proc Natl Acad Sci USA, 2003; 100(22): 12966–71.
-
(2003)
Proc Natl Acad Sci USA
, vol.100
, Issue.22
, pp. 12966-12971
-
-
Richards, A.1
Kemp, E.J.2
Liszewski, M.K.3
-
14
-
-
27744452766
-
Mutations in complement factor I predispose to development of atypical hemolytic uremic syndrome
-
Kavanagh D, Kemp EJ, Mayland E et al: Mutations in complement factor I predispose to development of atypical hemolytic uremic syndrome. J Am Soc Nephrol, 2005; 16(7): 2150–15.
-
(2005)
J am Soc Nephrol
, vol.16
, Issue.7
, pp. 2150-2215
-
-
Kavanagh, D.1
Kemp, E.J.2
Mayland, E.3
-
15
-
-
33747159590
-
Genetics of HUS: The impact of MCP, CFH, and IF mutations on clinical presentation, response to treatment, and outcome
-
Caprioli J, Noris M, Brioschi S et al: Genetics of HUS: the impact of MCP, CFH, and IF mutations on clinical presentation, response to treatment, and outcome. Blood, 2006; 108(4): 1267–79.
-
(2006)
Blood
, vol.108
, Issue.4
, pp. 1267-1279
-
-
Caprioli, J.1
Noris, M.2
Brioschi, S.3
-
16
-
-
75649133611
-
Association of factor H autoantibodies with deletions of CFHR1, CFHR3, CFHR4, and with mutations in CFH, CFI, CD46, and C3 in patients with atypical hemolytic uremic syndrome
-
Moore I, Strain L, Pappworth I et al: Association of factor H autoantibodies with deletions of CFHR1, CFHR3, CFHR4, and with mutations in CFH, CFI, CD46, and C3 in patients with atypical hemolytic uremic syndrome. Blood, 2010; 115(2): 379–87.
-
(2010)
Blood
, vol.115
, Issue.2
, pp. 379-387
-
-
Moore, I.1
Strain, L.2
Pappworth, I.3
-
17
-
-
34047200899
-
Deletion of complement factor H-related genes CFHR1 and CFHR3 is associated with atypical hemolytic uremic syndrome
-
e41
-
Zipfel PF, Edey M, Heinen S et al: Deletion of complement factor H-related genes CFHR1 and CFHR3 is associated with atypical hemolytic uremic syndrome. PLoS Genet, 2007; 3(3): e41.
-
(2007)
Plos Genet
, vol.3
, Issue.3
-
-
Zipfel, P.F.1
Edey, M.2
Heinen, S.3
-
18
-
-
33846094404
-
Gain-of-function mutations in complement factor B are associated with atypical hemolytic uremic syndrome
-
Goicoechea de Jorge E, Harris CL, Esparza-Gordillo J et al: Gain-of-function mutations in complement factor B are associated with atypical hemolytic uremic syndrome. Proc Natl Acad Sci USA, 2007; 104(1): 240–45.
-
(2007)
Proc Natl Acad Sci USA
, vol.104
, Issue.1
, pp. 240-245
-
-
De Goicoechea Jorge, E.1
Harris, C.L.2
Esparza-Gordillo, J.3
-
19
-
-
67651166873
-
Thrombomodulin mutations in atypical hemolytic-uremic syndrome
-
Delvaeye M, Noris M, De Vriese A et al: Thrombomodulin mutations in atypical hemolytic-uremic syndrome. N Engl J Med, 2009; 361(4): 345–57.
-
(2009)
N Engl J Med
, vol.361
, Issue.4
, pp. 345-357
-
-
Delvaeye, M.1
Noris, M.2
De Vriese, A.3
-
20
-
-
84883054621
-
Diagnosis of atypical hemolytic uremic syndrome: A review of case studies
-
Laurence J: Diagnosis of atypical hemolytic uremic syndrome: a review of case studies. Clin Adv Hematol Oncol, 2012; 10(10 Suppl.17): 9–11.
-
(2012)
Clin Adv Hematol Oncol
, vol.10
, Issue.10
, pp. 9-11
-
-
Laurence, J.1
-
21
-
-
77953008442
-
Myocardial infarction is a complication of factor H-associated atypical HUS
-
Sallée M, Daniel L, Piercecchi MD et al: Myocardial infarction is a complication of factor H-associated atypical HUS. Nephrol Dial Transplant, 2010; 25(6): 2028–32.
-
(2010)
Nephrol Dial Transplant
, vol.25
, Issue.6
, pp. 2028-2032
-
-
Sallée, M.1
Daniel, L.2
Piercecchi, M.D.3
-
22
-
-
78650517945
-
New insights into postrenal transplant hemolytic uremic syndrome
-
Zuber J, Le Quintrec M, Sberro-Soussan R et al: New insights into postrenal transplant hemolytic uremic syndrome. Nat Rev Nephrol, 2011; 7(1): 23–35.
-
(2011)
Nat Rev Nephrol
, vol.7
, Issue.1
, pp. 23-35
-
-
Zuber, J.1
Le Quintrec, M.2
Sberro-Soussan, R.3
-
23
-
-
0032956162
-
Thrombotic microangiopathy manifesting as thrombotic thrombocytopenic purpura/hemolytic uremic syndrome in the cancer patient
-
Gordon LI, Kwaan HC: Thrombotic microangiopathy manifesting as thrombotic thrombocytopenic purpura/hemolytic uremic syndrome in the cancer patient. Semin Thromb Hemost, 1999; 25(2): 217–21.
-
(1999)
Semin Thromb Hemost
, vol.25
, Issue.2
, pp. 217-221
-
-
Gordon, L.I.1
Kwaan, H.C.2
-
24
-
-
0028012915
-
Haemolytic-uraemic syndrome in practice
-
Neild GH: Haemolytic-uraemic syndrome in practice. Lancet, 1994; 343(8894): 398–401.
-
(1994)
Lancet
, vol.343
, Issue.8894
, pp. 398-401
-
-
Neild, G.H.1
-
25
-
-
22544461682
-
Hemolytic uremic syndrome
-
Noris, M, Remuzzi G: Hemolytic uremic syndrome. J Am Soc Nephrol, 2005; 16(4): 1035–50.
-
(2005)
J am Soc Nephrol
, vol.16
, Issue.4
, pp. 1035-1050
-
-
Noris, M.1
Remuzzi, G.2
-
26
-
-
84867993256
-
Use of eculizumab for atypical haemolytic uraemic syndrome and C3 glomerulopathies
-
Zuber J, Fakhouri F, Roumenina LT et al: Use of eculizumab for atypical haemolytic uraemic syndrome and C3 glomerulopathies. Nat Rev Nephrol, 2012; 8(11): 643–57.
-
(2012)
Nat Rev Nephrol
, vol.8
, Issue.11
, pp. 643-657
-
-
Zuber, J.1
Fakhouri, F.2
Roumenina, L.T.3
-
27
-
-
84874777659
-
Assesment, treatment and prevention of atypical hemolytic uremic syndrome
-
Nickavar A, Sotoudeh K: Assesment, treatment and prevention of atypical hemolytic uremic syndrome. Int J Prev Med, 2013; 4(1): 6–14.
-
(2013)
Int J Prev Med
, vol.4
, Issue.1
, pp. 6-14
-
-
Nickavar, A.1
Sotoudeh, K.2
-
28
-
-
79151471122
-
AHUS caused by complement dysregulation: New therapies on the horizon
-
Waters AM, Licht C: aHUS caused by complement dysregulation: new therapies on the horizon. Pediatr Nephrol, 2011; 26(1): 41–57.
-
(2011)
Pediatr Nephrol
, vol.26
, Issue.1
, pp. 41-57
-
-
Waters, A.M.1
Licht, C.2
-
29
-
-
34247381485
-
Complete factor H deficiency-associated atypical hemolytic uremic syndrome in a neonate
-
Cho HY, Lee BS, Moon KC et al: Complete factor H deficiency-associated atypical hemolytic uremic syndrome in a neonate. Pediatr Nephrol, 2007; 22(6): 874–80.
-
(2007)
Pediatr Nephrol
, vol.22
, Issue.6
, pp. 874-880
-
-
Cho, H.Y.1
Lee, B.S.2
Moon, K.C.3
-
30
-
-
59449088846
-
Eculizumab for congenital atypical hemolytic-uremic syndrome
-
Gruppo RA, Rother RP: Eculizumab for congenital atypical hemolytic-uremic syndrome. N Engl J Med, 2009; 360(5): 544–46.
-
(2009)
N Engl J Med
, vol.360
, Issue.5
, pp. 544-546
-
-
Gruppo, R.A.1
Rother, R.P.2
-
31
-
-
70349907791
-
Complement inhibitor eculizumab in atypical hemolytic uremic syndrome
-
Mache CJ, Acham-Roschitz B, Frémeaux-Bacchi V et al: Complement inhibitor eculizumab in atypical hemolytic uremic syndrome. Clin J Am Soc Nephrol, 2009; 4(8): 1312–16.
-
(2009)
Clin J am Soc Nephrol
, vol.4
, Issue.8
, pp. 1312-1316
-
-
Mache, C.J.1
Acham-Roschitz, B.2
Frémeaux-Bacchi, V.3
-
32
-
-
77956252835
-
Thrombotic microangiopathy: Atypical HUS: Current diagnostic and therapeutic approaches
-
Rosales A, Riedl M, Zimmerhackl LB: Thrombotic microangiopathy: atypical HUS: current diagnostic and therapeutic approaches. Nat Rev Nephrol, 2010; 6(9): 504–6.
-
(2010)
Nat Rev Nephrol
, vol.6
, Issue.9
, pp. 504-506
-
-
Rosales, A.1
Riedl, M.2
Zimmerhackl, L.B.3
-
33
-
-
81255130615
-
Eculizumab safely reverses neurologic impairment and eliminates need for dialysis in severe atypical hemolytic uremic syndrome
-
Ohanian M, Cable C, Halka K: Eculizumab safely reverses neurologic impairment and eliminates need for dialysis in severe atypical hemolytic uremic syndrome. Clin Pharmacol, 2011; 3: 5–12.
-
(2011)
Clin Pharmacol
, vol.3
, pp. 5-12
-
-
Ohanian, M.1
Cable, C.2
Halka, K.3
-
34
-
-
78649513705
-
Eculizumab therapy in an adult with plasma exchange-refractory atypical hemolytic uremic syndrome
-
Prescott HC, Wu HM, Cataland SR, Baiocchi RA et al: Eculizumab therapy in an adult with plasma exchange-refractory atypical hemolytic uremic syndrome. Am J Hematol, 2010; 85(12): 976–77.
-
(2010)
Am J Hematol
, vol.85
, Issue.12
, pp. 976-977
-
-
Prescott, H.C.1
Wu, H.M.2
Cataland, S.R.3
Baiocchi, R.A.4
-
35
-
-
84906522458
-
[Eculizumab for the treatment of atypical hemolytic uremic syndrome: Case report and revision of the literature.]
-
[in Portuguese]
-
Vaisbich MH, Henriques Ldos S, Watanabe A et al: [Eculizumab for the treatment of atypical hemolytic uremic syndrome: case report and revision of the literature.] J Bras Nefrol, 2013; 35(3): 237–41 [in Portuguese].
-
(2013)
J Bras Nefrol
, vol.35
, Issue.3
, pp. 237-241
-
-
Vaisbich, M.H.1
Henriques Ldos, S.2
Watanabe, A.3
-
36
-
-
84890548424
-
Long-term remission of atypical HUS with anti-factor H antibodies after cyclophosphamide pulses
-
Sana G, Dragon-Durey MA, Charbit M et al: Long-term remission of atypical HUS with anti-factor H antibodies after cyclophosphamide pulses. Pediatr Nephrol, 2014; 29(1): 75–83.
-
(2014)
Pediatr Nephrol
, vol.29
, Issue.1
, pp. 75-83
-
-
Sana, G.1
Dragon-Durey, M.A.2
Charbit, M.3
|