Laboratory diagnosis of Niemann-Pick disease type C: The filipin staining test

Methods in Cell Biology

Volumn 126, Issue , 2015, Pages 357-375

  Vanier, Marie T ^a   Latour, Philippe ^a  

^a HOSPICES CIVILS DE LYON   (France)

Author keywords

Cholesterol homeostasis; Filipin; Intracellular cholesterol; Intracellular trafficking; Laboratory diagnosis; Late endosome; Lysosome; Niemann Pick C disease; NPC1; NPC2

Indexed keywords

BIOLOGICAL MARKER; FILIPIN; LOW DENSITY LIPOPROTEIN CHOLESTEROL;

ANIMAL; BLOOD; CELL CULTURE; HUMAN; METABOLISM; NIEMANN-PICK DISEASE, TYPE C; STAINING;

ANIMALS; BIOLOGICAL MARKERS; CELLS, CULTURED; CHOLESTEROL, LDL; FILIPIN; HUMANS; NIEMANN-PICK DISEASE, TYPE C; STAINING AND LABELING;

EID: 84922941577     PISSN: 0091679X     EISSN: None     Source Type: Book Series    
DOI: 10.1016/bs.mcb.2014.10.028     Document Type: Article

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