Not all (bile acids) who wander are lost: The first report of a patient with an isolated NTCP defect

Hepatology

Volumn 61, Issue 1, 2015, Pages 24-27

  Karpen, Saul J ^a   Dawson, Paul A ^a  

^a EMORY UNIVERSITY SCHOOL OF MEDICINE   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

BILE ACID; BILE ACID CONJUGATE; FIBROBLAST GROWTH FACTOR 19; SODIUM BILE ACID COTRANSPORTER; SOLUTE CARRIER ORGANIC ANION TRANSPORTER 1B1; CHOLIC ACID DERIVATIVE; COTRANSPORTER; ORGANIC ANION TRANSPORTER; SODIUM-BILE ACID COTRANSPORTER;

ABNORMALLY HIGH SUBSTRATE CONCENTRATION IN BLOOD; ARTICLE; BILE ACID BLOOD LEVEL; BILE ACID METABOLISM; BILE ACID SYNTHESIS; CHOLELITHIASIS; CHOLESTASIS; ENTEROHEPATIC CIRCULATION; HEPATOBILIARY DISEASE; HUMAN; HYPERCHOLANEMIA; INTESTINAL REABSORPTION; INTRAHEPATIC CHOLESTASIS; LIPID TRANSPORT; LIVER CLEARANCE; LIVER FUNCTION; MALABSORPTION; PRIORITY JOURNAL; PRURITUS; SINGLE NUCLEOTIDE POLYMORPHISM; BLOOD; DEFICIENCY; FEMALE; GENETICS; INBORN ERROR OF STEROID METABOLISM;

CHOLIC ACIDS; FEMALE; HUMANS; ORGANIC ANION TRANSPORTERS, SODIUM-DEPENDENT; STEROID METABOLISM, INBORN ERRORS; SYMPORTERS;

EID: 84920973434     PISSN: 02709139     EISSN: 15273350     Source Type: Journal    
DOI: 10.1002/hep.27294     Document Type: Article

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