Glycogen phosphomonoester distribution in mouse models of the progressive myoclonic epilepsy, Lafora disease

Journal of Biological Chemistry

Volumn 290, Issue 2, 2015, Pages 841-850

  DePaoli Roach, Anna A ^a   Contreras, Christopher J ^a   Segvich, Dyann M ^a   Heiss, Christian ^b   Ishihara, Mayumi ^b   Azadi, Parastoo ^b   Roach, Peter J ^b  

^a INDIANA UNIVERSITY SCHOOL OF MEDICINE   (United States)

^b UNIVERSITY OF GEORGIA   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

GENES; GLUCOSE; MUSCLE; NEUROLOGY; PHOSPHORYLATION;

BRANCHED POLYMER; ENERGY RESERVES; GENETIC DISEASE; GLUCOSE RESIDUES; HYPERPHOSPHORYLATED; MUSCLE GLYCOGENS; SENSITIVE ASSAY; SKELETAL MUSCLE;

MAMMALS;

ESTER DERIVATIVE; GLUCOSE 6 PHOSPHATASE; GLYCOGEN; GLYCOGEN PHOSPHOMONOESTER; PHOSPHATE; UNCLASSIFIED DRUG; DUAL SPECIFICITY PHOSPHATASE; EPM2A PROTEIN, MOUSE; GLUCOSE 6 PHOSPHATE; NHLRC1 PROTEIN, MOUSE; UBIQUITIN PROTEIN LIGASE;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CARBOHYDRATE ANALYSIS; CHEMICAL STRUCTURE; CONCENTRATION (PARAMETERS); CONTROLLED STUDY; GLYCOGEN DISTRIBUTION; GLYCOGEN METABOLISM; GLYCOGEN PHOSPHORYLATION; KNOCKOUT MOUSE; MOUSE; MOUSE MODEL; MYOCLONUS EPILEPSY; NONHUMAN; NUCLEAR MAGNETIC RESONANCE SPECTROSCOPY; PHOSPHORYLATION; RABBIT; SKELETAL MUSCLE; WILD TYPE MOUSE; ANIMAL; CHEMISTRY; DISEASE MODEL; GENETICS; HUMAN; METABOLISM; MUTATION; PATHOLOGY; TRANSGENIC MOUSE;

MUS; ORYCTOLAGUS CUNICULUS;

ANIMALS; DISEASE MODELS, ANIMAL; DUAL-SPECIFICITY PHOSPHATASES; GLUCOSE-6-PHOSPHATE; GLYCOGEN; HUMANS; LAFORA DISEASE; MICE; MICE, TRANSGENIC; MUTATION; PHOSPHORYLATION; RABBITS; UBIQUITIN-PROTEIN LIGASES;

EID: 84920887582     PISSN: 00219258     EISSN: 1083351X     Source Type: Journal    
DOI: 10.1074/jbc.M114.607796     Document Type: Article

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