LMO7-null mice exhibit phenotypes consistent with emery-dreifuss muscular dystrophy

Muscle and Nerve

Volumn 51, Issue 2, 2015, Pages 222-228

  Mull, Aaron ^a   Kim, Gene ^a   Holaska, James M ^a,b  

^a Pritzker School of Medicine   (United States)

^b UNIVERSITY OF THE SCIENCES   (United States)

Author keywords

Emerin; Emery Dreifuss muscular dystrophy; Lmo7; Nuclear envelope; Nucleoskeleton

Indexed keywords

LIM PROTEIN; LMO7 PROTEIN, MOUSE; MITOGEN ACTIVATED PROTEIN KINASE; TRANSCRIPTION FACTOR;

ANIMAL; BODY MASS; BODY WEIGHT; C57BL MOUSE; DEFICIENCY; DISEASE MODEL; ECHOCARDIOGRAPHY; EMERY DREIFUSS MUSCULAR DYSTROPHY; GENE EXPRESSION REGULATION; GENETICS; HEART DISEASE; HUMAN; KNOCKOUT MOUSE; METABOLISM; MOUSE; MUSCLE CONTRACTION; NEUROMUSCULAR JUNCTION DISEASES; PATHOPHYSIOLOGY; PHENOTYPE; PHYSIOLOGY; SIGNAL TRANSDUCTION; SKELETAL MUSCLE;

ANIMALS; BODY MASS INDEX; BODY WEIGHT; DISEASE MODELS, ANIMAL; ECHOCARDIOGRAPHY; GENE EXPRESSION REGULATION; HEART DISEASES; HUMANS; LIM DOMAIN PROTEINS; MICE; MICE, INBRED C57BL; MICE, KNOCKOUT; MITOGEN-ACTIVATED PROTEIN KINASES; MUSCLE CONTRACTION; MUSCLE, SKELETAL; MUSCULAR DYSTROPHY, EMERY-DREIFUSS; NEUROMUSCULAR JUNCTION DISEASES; PHENOTYPE; SIGNAL TRANSDUCTION; TRANSCRIPTION FACTORS;

EID: 84920876070     PISSN: 0148639X     EISSN: 10974598     Source Type: Journal    
DOI: 10.1002/mus.24286     Document Type: Article

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