Early white matter changes in CADASIL: Evidence of segmental intramyelinic oedema in a pre-clinical mouse model

Acta Neuropathologica Communications

Volumn 2, Issue 1, 2014, Pages

  Cognat, Emmanuel ^a   Cleophax, Sabine ^a   Domenga Denier, Valérie ^a   Joutel, Anne ^a  

^a INSERM   (France)

Author keywords

CADASIL; Intramyelinic oedema; Mouse model; Small vessel disease; White matter

Indexed keywords

ACTIN BINDING PROTEIN; AIF1 PROTEIN, MOUSE; BASIC HELIX LOOP HELIX TRANSCRIPTION FACTOR; CALCIUM BINDING PROTEIN; CD68 ANTIGEN, HUMAN; DIFFERENTIATION ANTIGEN; LEUKOCYTE ANTIGEN; NERVE PROTEIN; NOTCH RECEPTOR; NOTCH3 PROTEIN, MOUSE; OLIG2 PROTEIN, MOUSE;

AGE; ANIMAL; BRAIN EDEMA; CADASIL; CELL VACUOLE; COMPLICATION; DISEASE COURSE; DISEASE MODEL; ELECTRON MICROSCOPY; GENE EXPRESSION REGULATION; GENETICS; LEUKOENCEPHALOPATHIES; METABOLISM; MICROGLIA; MOUSE; MUTATION; MYELIN SHEATH; NERVE FIBER; PATHOLOGY; TRANSGENIC MOUSE; ULTRASTRUCTURE;

AGE FACTORS; ANIMALS; ANTIGENS, CD; ANTIGENS, DIFFERENTIATION, MYELOMONOCYTIC; AXONS; BASIC HELIX-LOOP-HELIX TRANSCRIPTION FACTORS; BRAIN EDEMA; CADASIL; CALCIUM-BINDING PROTEINS; DISEASE MODELS, ANIMAL; DISEASE PROGRESSION; GENE EXPRESSION REGULATION; LEUKOENCEPHALOPATHIES; MICE; MICE, TRANSGENIC; MICROFILAMENT PROTEINS; MICROGLIA; MICROSCOPY, ELECTRON; MUTATION; MYELIN SHEATH; NERVE TISSUE PROTEINS; RECEPTORS, NOTCH; VACUOLES;

EID: 84920499368     PISSN: None     EISSN: 20515960     Source Type: Journal    
DOI: 10.1186/2051-5960-2-49     Document Type: Article

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