Characterization of the MeCP2R168X knockin mouse model for Rett syndrome

PLoS ONE

Volumn 9, Issue 12, 2014, Pages

  Wegener, Eike ^a   Brendel, Cornelia ^a   Fischer, Andre ^a,b   Hülsmann, Swen ^c   Gärtner, Jutta ^a   Huppke, Peter ^a  

^a UNIVERSITY MEDICAL CENTER GÖTTINGEN   (Germany)

^b GERMAN CENTER FOR NEURODEGENERATIVE DISEASES DZNE   (Germany)

^c Center for Nanoscale Microscopy and Molecular Physiology of the Brain (CNMPB)   (Germany)

Author keywords

[No Author keywords available]

Indexed keywords

ALLELE; ANIMAL EXPERIMENT; ANIMAL MODEL; ANXIETY; APNEA; ARTICLE; CONTROLLED STUDY; ELEVATED PLUS MAZE TEST; GENE MUTATION; HINDLIMB; MALE; MENTAL DEFICIENCY; MOTOR PERFORMANCE; MOUSE; NESTING; NONHUMAN; NONSENSE MUTATION; OPEN FIELD TEST; PHENOTYPE; PLETHYSMOGRAPHY; RETT SYNDROME; ROTAROD TEST; SYMPTOMATOLOGY; TRANSLATIONAL RESEARCH; TREMOR; WILD TYPE; ANIMAL; DISEASE MODEL; FEMALE; GENE TARGETING; GENETICS; HUMAN; PATHOLOGY; PATHOPHYSIOLOGY; SEX DIFFERENCE; STOP CODON;

MUS;

MECP2 PROTEIN, MOUSE; METHYL CPG BINDING PROTEIN 2; STOP CODON;

ANIMALS; CODON, NONSENSE; DISEASE MODELS, ANIMAL; FEMALE; GENE KNOCK-IN TECHNIQUES; HUMANS; MALE; METHYL-CPG-BINDING PROTEIN 2; MICE; PHENOTYPE; RETT SYNDROME; SEX FACTORS; TRANSLATIONAL MEDICAL RESEARCH;

EID: 84919912967     PISSN: None     EISSN: 19326203     Source Type: Journal    
DOI: 10.1371/journal.pone.0115444     Document Type: Article

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