Severe hypercholesterolemia and phytosterolemia with extensive xanthomas in primary biliary cirrhosis: Role of biliary excretion on sterol homeostasis

Journal of Clinical Lipidology

Volumn 8, Issue 5, 2014, Pages 520-524

  Baila Rueda, Lucia ^a   Mateo Gallego, Rocio ^a   Lamiquiz Moneo, Itziar ^a   Cenarro, Ana ^a   Civeira, Fernando ^a  

^a HOSPITAL UNIVERSITARIO MIGUEL SERVET   (Spain)

Author keywords

Hypercholesterolemia; Phytosterolemia; Primary biliary cirrhosis; Xanthomas

Indexed keywords

ALKALINE PHOSPHATASE; APOLIPOPROTEIN B; BILIRUBIN GLUCURONIDE; EZETIMIBE; FENOFIBRATE; HIGH DENSITY LIPOPROTEIN CHOLESTEROL; LIPOPROTEIN X; PHYTOSTEROL; ROSUVASTATIN; STEROL; TRIACYLGLYCEROL;

ADULT; ARTICLE; BILE SECRETION; BILIARY EXCRETION; CASE REPORT; CHOLESTASIS; CHOLESTEROL BLOOD LEVEL; DISORDERS OF LIPID AND LIPOPROTEIN METABOLISM; DNA SEQUENCE; EOSINOPHIL; FAST PROTEIN LIQUID CHROMATOGRAPHY; FEMALE; GENE AMPLIFICATION; GENETIC VARIABILITY; HIGH PERFORMANCE LIQUID CHROMATOGRAPHY; HOMEOSTASIS; HUMAN; HUMAN TISSUE; HYPERCHOLESTEROLEMIA; JAUNDICE; LIPID STORAGE; LIVER BIOPSY; LYMPHOCYTE; NEUTROPHIL; PHYTOSTEROLEMIA; PRIMARY BILIARY CIRRHOSIS; PRURITUS; THROMBOCYTE COUNT; THROMBOCYTE VOLUME; XANTHOMA; BILIARY CIRRHOSIS; COMPLICATION; ENTEROPATHY; HEPATOBILIARY SYSTEM; METABOLISM; SECRETION (PROCESS); XANTHOMATOSIS;

ADULT; BILIARY TRACT; FEMALE; HOMEOSTASIS; HUMANS; HYPERCHOLESTEROLEMIA; INTESTINAL DISEASES; LIPID METABOLISM, INBORN ERRORS; LIVER CIRRHOSIS, BILIARY; PHYTOSTEROLS; STEROLS; XANTHOMATOSIS;

EID: 84908897546     PISSN: 19332874     EISSN: 18764789     Source Type: Journal    
DOI: 10.1016/j.jacl.2014.05.004     Document Type: Article

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