Hepatocyte transplantation ameliorates the metabolic abnormality in a mouse model of acute intermittent porphyria

Cell Transplantation

Volumn 23, Issue 9, 2014, Pages 1153-1162

  Yin, Zhaohui ^a,b   Wahlin, Staffan ^a   Ellis, Ewa C S ^a   Harper, Pauline ^a   Ericzon, Bo Göran ^a   Nowak, Greg ^a  

^a KAROLINSKA UNIVERSITY HOSPITAL   (Sweden)

^b THE FIRST AFFILIATED HOSPITAL OF SHANTOU UNIVERSITY MEDICAL COLLEGE   (China)

Author keywords

Acute intermittent porphyria (AIP); Hepatocyte transplantation; Mice; Porphobilinogen deaminase (PBGD)

Indexed keywords

5 AMINOLEVULINATE SYNTHASE; AMINOLEVULINIC ACID; CHLORMETHINE; CYTOCHROME P450 2A5; MESSENGER RNA; PHENOBARBITAL; PORPHOBILINOGEN; PORPHOBILINOGEN DEAMINASE; CYP2A5 PROTEIN, MOUSE; UNSPECIFIC MONOOXYGENASE;

ACUTE INTERMITTENT PORPHYRIA; ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CELL MEMBRANE; CONTROLLED STUDY; ENGRAFTMENT; ENZYME ACTIVITY; FEMALE; GENETIC TRANSCRIPTION; HEME SYNTHESIS; HEPATOCYTE TRANSPLANTATION; LIVER CELL; LIVER RESECTION; MALE; MOTOR PERFORMANCE; MOUSE; MUSCLE CELL; NONHUMAN; NUCLEOTIDE SEQUENCE; QUADRICEPS FEMORIS MUSCLE; REVERSE TRANSCRIPTION POLYMERASE CHAIN REACTION; WILD TYPE; ALLOTRANSPLANTATION; ANIMAL; BLOOD; C57BL MOUSE; CELL CULTURE; CYTOLOGY; DISEASE MODEL; GENETICS; METABOLISM; PORPHYRIA, ACUTE INTERMITTENT; TRANSPLANTATION;

5-AMINOLEVULINATE SYNTHETASE; AMINOLEVULINIC ACID; ANIMALS; ARYL HYDROCARBON HYDROXYLASES; CELLS, CULTURED; DISEASE MODELS, ANIMAL; HEPATOCYTES; HYDROXYMETHYLBILANE SYNTHASE; MALE; MICE; MICE, INBRED C57BL; PORPHOBILINOGEN; PORPHYRIA, ACUTE INTERMITTENT; RNA, MESSENGER; TRANSPLANTATION, HOMOLOGOUS;

EID: 84906962047     PISSN: 09636897     EISSN: None     Source Type: Journal    
DOI: 10.3727/096368913X666980     Document Type: Article

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