One liver for four children: First clinical series of liver cell transplantation for severe neonatal urea cycle defects

Transplantation

Volumn 87, Issue 5, 2009, Pages 636-641

  Meyburg, Jochen ^a   Das, Anibh M ^b   Hoerster, Friederike ^a   Lindner, Martin ^a   Kriegbaum, Heinz ^c   Engelmann, Guido ^a   Schmidt, Jan ^a   Ott, Michael ^b   Pettenazzo, Andrea ^d   Luecke, Thomas ^b   Bertram, Harald ^b   Hoffmann, Georg F ^a   Burlina, Alberto ^d  

^a UNIVERSITY HOSPITAL HEIDELBERG   (Germany)

^b HANNOVER MEDICAL SCHOOL   (Germany)

^c Cytonet GmbH and Co KG   (Germany)

^d UNIVERSITY HOSPITAL OF PADOVA   (Italy)

Author keywords

Carbamoylphosphate synthase deficiency; Citrullinaemia; Cryopreserved hepatocytes; Hepatocyte transplantation; Ornithine transcarbamylase deficiency

Indexed keywords

ALLOPURINOL; AMMONIA; BASILIXIMAB; CARBAMOYL PHOSPHATE SYNTHASE; CYCLOSPORIN A; METHYLPREDNISOLONE; ORNITHINE CARBAMOYLTRANSFERASE; OROTIC ACID; PREDNISOLONE; TACROLIMUS; UREA;

AMMONIA BLOOD LEVEL; ARTICLE; CASE REPORT; CHILD; CITRULLINEMIA; CRYOPRESERVATION; DISORDERS OF AMINO ACID AND PROTEIN METABOLISM; FEMALE; HEPATOCYTE TRANSPLANTATION; HUMAN; HYPERAMMONEMIA; IMMUNOSUPPRESSIVE TREATMENT; INFANT; LIVER GRAFT REJECTION; MALE; NEWBORN; ORGAN DONOR; OUTCOME ASSESSMENT; PRESCHOOL CHILD; PRIORITY JOURNAL; TREATMENT INDICATION; UREA BLOOD LEVEL; UREA CYCLE; BLOOD; CELL TRANSPLANTATION; DONOR; LIVER CELL; LIVER TRANSPLANTATION; METABOLISM; METHODOLOGY; PORTAL VEIN; TRANSPLANTATION; TREATMENT OUTCOME;

AMMONIA; CELL TRANSPLANTATION; CRYOPRESERVATION; HEPATOCYTES; HUMANS; INFANT; INFANT, NEWBORN; LIVER TRANSPLANTATION; ORNITHINE CARBAMOYLTRANSFERASE DEFICIENCY DISEASE; PORTAL VEIN; TISSUE DONORS; TREATMENT OUTCOME; UREA;

EID: 65649095157     PISSN: 00411337     EISSN: None     Source Type: Journal    
DOI: 10.1097/TP.0b013e318199936a     Document Type: Article

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