Time course of pathogenic and adaptation mechanisms in cystinotic mouse kidneys

Journal of the American Society of Nephrology

Volumn 25, Issue 6, 2014, Pages 1256-1269

  Gaide Chevronnay, Héloïse P ^a   Janssens, Virginie ^a   Van Der Smissen, Patrick ^a   N'Kuli, Francisca ^a   Nevo, Nathalie ^b   Guiot, Yves ^c   Levtchenko, Elena ^d   Marbaix, Etienne ^a,c   Pierreux, Christophe E ^a   Cherqui, Stéphanie ^e   Antignac, Corinne ^b   Courtoy, Pierre J ^a  

^a UNIVERSITÉ CATHOLIQUE DE LOUVAIN   (Belgium)

^b IMAGINE INSTITUTE   (France)

^c CLINIQUES UNIVERSITAIRES SAINT LUC   (Belgium)

^d UNIVERSITY HOSPITALS LEUVEN   (Belgium)

^e UNIVERSITY OF CALIFORNIA SAN DIEGO   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

AQUAPORIN 2; CUBILIN; CYSTINE; CYSTINOSIN; DISULFIDE; HYPOXANTHINE PHOSPHORIBOSYLTRANSFERASE; MEGALIN; PODOCIN; PROTEIN; SODIUM GLUCOSE COTRANSPORTER 2; SODIUM PHOSPHATE COTRANSPORTER 2A; UNCLASSIFIED DRUG; AMINO ACID TRANSPORTER; CELL SURFACE RECEPTOR; CYSTINOSIN PROTEIN, MOUSE; INTRINSIC FACTOR COBALAMIN RECEPTOR; INTRINSIC FACTOR-COBALAMIN RECEPTOR; LRP2 PROTEIN, MOUSE;

ADAPTATION; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; APOPTOSIS; ARTICLE; ATROPHY; CELL DEDIFFERENTIATION; CELL VACUOLE; CHILD; CLINICAL ARTICLE; CONTROLLED STUDY; CYSTINOSIS; ENDOCYTOSIS; ENZYMURIA; FANCONI RENOTUBULAR SYNDROME; GENE EXPRESSION; HUMAN; IMMUNOFLUORESCENCE MICROSCOPY; IN SITU HYBRIDIZATION; KIDNEY CLEARANCE; KIDNEY PROXIMAL TUBULE; KIDNEY TUBULE CELL; KNOCKOUT MOUSE; MOUSE; MULTIPHOTON MICROSCOPY; NEPHRON; NONHUMAN; PRIORITY JOURNAL; PROTEIN EXPRESSION; PROTEINURIA; ANIMAL; C57BL MOUSE; CELL PROLIFERATION; CHEMISTRY; CRYSTALLIZATION; DISEASE COURSE; DISEASE MODEL; GENETICS; LYSOSOME; METABOLISM; PATHOLOGY; PATHOPHYSIOLOGY; PHYSIOLOGY;

ADAPTATION, PHYSIOLOGICAL; AMINO ACID TRANSPORT SYSTEMS, NEUTRAL; ANIMALS; APOPTOSIS; CELL PROLIFERATION; CRYSTALLIZATION; CYSTINE; CYSTINOSIS; DISEASE MODELS, ANIMAL; DISEASE PROGRESSION; ENDOCYTOSIS; FANCONI SYNDROME; KIDNEY TUBULES, PROXIMAL; LOW DENSITY LIPOPROTEIN RECEPTOR-RELATED PROTEIN-2; LYSOSOMES; MICE; MICE, INBRED C57BL; MICE, KNOCKOUT; PROTEINURIA; RECEPTORS, CELL SURFACE; VACUOLES;

EID: 84906079486     PISSN: 10466673     EISSN: 15333450     Source Type: Journal    
DOI: 10.1681/ASN.2013060598     Document Type: Article

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