Dietary triheptanoin rescues oligodendrocyte loss, dysmyelination and motor function in the nur7 mouse model of Canavan disease

Journal of Inherited Metabolic Disease

Volumn 37, Issue 3, 2014, Pages 369-381

  Francis, Jeremy S ^a   Markov, Vladimir ^a   Leone, Paola ^a  

^a UMDNJ School of Osteopathic Medicine   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

MYELIN; TRIHEPTANOIN; ADENOSINE TRIPHOSPHATE; AMIDASE; ASPARTIC ACID; ASPARTOACYLASE; N-ACETYLASPARTATE; TRIACYLGLYCEROL;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CANAVAN DISEASE; CELL LOSS; CELL SURVIVAL; CONTROLLED STUDY; DIET THERAPY; MOTOR PERFORMANCE; MOUSE; MOUSE MODEL; MYELINATION; NEWBORN; NONHUMAN; OLIGODENDROGLIA; OXIDATIVE STRESS; REDUCTION; ANALOGS AND DERIVATIVES; ANIMAL; DISEASE MODEL; GENETICS; METABOLISM; MYELIN SHEATH; PATHOLOGY; PATHOPHYSIOLOGY; PHYSIOLOGY;

ADENOSINE TRIPHOSPHATE; AMIDOHYDROLASES; ANIMALS; ASPARTIC ACID; CANAVAN DISEASE; DISEASE MODELS, ANIMAL; MICE; MYELIN SHEATH; OLIGODENDROGLIA; TRIGLYCERIDES;

EID: 84904196534     PISSN: 01418955     EISSN: 15732665     Source Type: Journal    
DOI: 10.1007/s10545-013-9663-6     Document Type: Article

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