Ube3a, the E3 ubiquitin ligase causing Angelman syndrome and linked to autism, regulates protein homeostasis through the proteasomal shuttle Rpn10

Cellular and Molecular Life Sciences

Volumn 71, Issue 14, 2014, Pages 2747-2758

  Lee, So Young ^a   Ramirez, Juanma ^a   Franco, Maribel ^a,c   Lectez, Benoît ^a   Gonzalez, Monika ^a   Barrio, Rosa ^a   Mayor, Ugo ^a,b  

^a CIC BIOGUNE   (Spain)

^b BASQUE FOUNDATION FOR SCIENCE   (Spain)

^c INSTITUTO DE NEUROCIENCIAS   (Spain)

Author keywords

Angelman syndrome; Autism; Proteasome; Rpn10; Ube3a; Ubiquitin

Indexed keywords

UBIQUITIN PROTEIN LIGASE E3; UBIQUITIN PROTEIN LIGASE E3 UBE3A; UNCLASSIFIED DRUG;

AMINO TERMINAL SEQUENCE; ANIMAL CELL; ARTICLE; AUTISM; BINDING AFFINITY; CARBOXY TERMINAL SEQUENCE; CELL DIFFERENTIATION; CELL PROLIFERATION; CONFOCAL MICROSCOPY; CONTROLLED STUDY; DISEASE ASSOCIATION; DROSOPHILA; HAPPY PUPPET SYNDROME; HOMEOSTASIS; IMMUNOBLOTTING; NONHUMAN; PROTEIN BINDING; PROTEIN DEGRADATION; PROTEIN DENATURATION; PROTEIN LOCALIZATION; PROTEIN PROCESSING; PROTEIN PROTEIN INTERACTION; PROTEIN PURIFICATION; PROTEOMICS; START CODON; UBIQUITINATION;

ANGELMAN SYNDROME; ANIMALS; CARRIER PROTEINS; DROSOPHILA; DROSOPHILA PROTEINS; HOMEOSTASIS; HUMANS; PROTEIN INTERACTION MAPPING; PROTEIN TRANSPORT; UBIQUITIN-PROTEIN LIGASES; UBIQUITINATION;

EID: 84903269479     PISSN: 1420682X     EISSN: 14209071     Source Type: Journal    
DOI: 10.1007/s00018-013-1526-7     Document Type: Article

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