Improvement of cardiac function by short-term enzyme replacement therapy in a murine model of cardiomyopathy associated with Hunter syndrome evaluated by serial echocardiography with speckle tracking 2-D strain analysis

Molecular Genetics and Metabolism

Volumn 112, Issue 3, 2014, Pages 218-223

  Lee, Sang Chol ^a   Lee, Jieun ^a   Jin, Dong Kyu ^a   Kim, Jung Sun ^a   Jeon, Eun Seok ^a   Kwun, Young Hee ^a   Chang, Mi Sun ^a   Ko, Ah ra ^b   Yook, Yeon Joo ^b   Sohn, Young Bae ^c  

^a Sungkyunkwan University School of Medicine   (South Korea)

^b Samsung Advanced Institute of Technology (SAIT)   (South Korea)

^c Ajou University School of Medicine   (South Korea)

Author keywords

Echocardiography; Enzyme replacement; Mucopolysaccharidosis; Speckle tracking; Strain

Indexed keywords

IDURONATE 2 SULFATASE;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CARDIOMYOPATHY; CONTROLLED STUDY; DRUG EFFECT; DRUG EFFICACY; ECHOCARDIOGRAPHY; ENZYME REPLACEMENT; FEMALE; FOLLOW UP; HEART FUNCTION; HEART LEFT VENTRICLE CONTRACTION; HEART LEFT VENTRICLE FUNCTION; HEART LEFT VENTRICLE SIZE; HEART MUSCLE FIBROSIS; HISTOLOGY; HUNTER SYNDROME; KNOCKOUT MOUSE; MALE; MOUSE; NONHUMAN; PRIORITY JOURNAL; SPECKLE TRACKING ECHOCARDIOGRAPHY; ANIMAL; CARDIOMYOPATHIES; COMPLICATION; DISEASE MODEL; MUCOPOLYSACCHARIDOSIS II; PATHOPHYSIOLOGY; TREATMENT OUTCOME;

MURINAE; MUS;

ANIMALS; CARDIOMYOPATHIES; DISEASE MODELS, ANIMAL; ECHOCARDIOGRAPHY; ENZYME REPLACEMENT THERAPY; FEMALE; IDURONATE SULFATASE; MALE; MICE; MICE, KNOCKOUT; MUCOPOLYSACCHARIDOSIS II; TREATMENT OUTCOME; VENTRICULAR DYSFUNCTION, LEFT;

EID: 84902551355     PISSN: 10967192     EISSN: 10967206     Source Type: Journal    
DOI: 10.1016/j.ymgme.2014.04.005     Document Type: Article

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