Co-existence of clonal expanded autologous and transplacental-acquired maternal T cells in recombination activating gene-deficient severe combined immunodeficiency

Clinical and Experimental Immunology

Volumn 176, Issue 3, 2014, Pages 380-386

  Lev, A ^a,b   Simon, A J ^a,b   Ben Ari, J ^a,c   Takagi, D ^a,c   Stauber, T ^a,c   Trakhtenbrot, L ^a,b   Rosenthal, E ^a,b   Rechavi, G ^a,b   Amariglio, N ^a,b   Somech, R ^a,b  

^a TEL AVIV UNIVERSITY   (Israel)

^b SHEBA MEDICAL CENTER   (Israel)

^c MEIR MEDICAL CENTER   (Israel)

Author keywords

Maternal engraftment; Omenn syndrome; RAG1; SCID; T cell receptor repertoire

Indexed keywords

HLA B ANTIGEN; HLA B50 ANTIGEN; T LYMPHOCYTE RECEPTOR BETA CHAIN; T LYMPHOCYTE RECEPTOR GAMMA CHAIN; UNCLASSIFIED DRUG;

ARTICLE; CASE REPORT; CELL COUNT; CELL POPULATION; CLONAL VARIATION; CONTROLLED STUDY; GENE; GENE REARRANGEMENT; HUMAN; HUMAN CELL; MALE; OMENN SYNDROME; PRIORITY JOURNAL; RAG1 GENE; REGULATORY T LYMPHOCYTE; SEVERE COMBINED IMMUNODEFICIENCY; T LYMPHOCYTE;

MATERNAL ENGRAFTMENT; OMENN SYNDROME; RAG1; SCID; T CELL RECEPTOR REPERTOIRE;

CLONAL EVOLUTION; DNA MUTATIONAL ANALYSIS; HOMEODOMAIN PROTEINS; HUMANS; IMMUNOPHENOTYPING; MUTATION; PHENOTYPE; RECEPTORS, ANTIGEN, T-CELL, ALPHA-BETA; RECEPTORS, ANTIGEN, T-CELL, GAMMA-DELTA; SEVERE COMBINED IMMUNODEFICIENCY; T-LYMPHOCYTE SUBSETS;

EID: 84899091809     PISSN: 00099104     EISSN: 13652249     Source Type: Journal    
DOI: 10.1111/cei.12273     Document Type: Article

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