Role of cholesterol sulfate in epidermal structure and function: Lessons from X-linked ichthyosis

Biochimica et Biophysica Acta - Molecular and Cell Biology of Lipids

Volumn 1841, Issue 3, 2014, Pages 353-361

  Elias, Peter M ^a   Williams, Mary L ^b   Choi, Eung Ho ^c   Feingold, Kenneth R ^b  

^a VETERANS AFFAIRS MEDICAL CENTER   (United States)

^b UNIVERSITY OF CALIFORNIA   (United States)

^c Yonsei University Wonju   (South Korea)

Author keywords

Cholesterol sulfate; Corneodesmosomes; Epidermal barrier function; Epidermal lipid metabolism; Steroid sulfatase; X linked ichthyosis

Indexed keywords

ARYLSULFATASE; CHOLESTEROL; CHOLESTEROL SULFATE; INTERLEUKIN 1BETA; INTERLEUKIN 6; KALLIKREIN 5; LIPID; STERYL SULFATASE; STRATUM CORNEUM CHYMOTRYPTIC ENZYME; SULFOTRANSFERASE;

CELL DIFFERENTIATION; CHOLESTEROL SYNTHESIS; CHROMOSOME DELETION X; CLINICAL FEATURE; DESQUAMATION; ENZYME ACTIVITY; ENZYME LOCALIZATION; ENZYME REGULATION; EPIDERMIS; EPIDERMIS HYPERPLASIA; EXTRACELLULAR MATRIX; HUMAN; HYPERKERATOSIS; KERATINOCYTE; LAMELLAR BODY; MALE TYPE ALOPECIA; MAROTEAUX LAMY SYNDROME; MOLECULAR BIOLOGY; NEWBORN PERIOD; NONHUMAN; PATHOGENESIS; PERMEABILITY BARRIER; PHENOTYPE; PRIORITY JOURNAL; PROTEIN LOCALIZATION; REVIEW; SKIN FUNCTION; SKIN STRUCTURE; STEROL ANALYSIS; STRATUM CORNEUM; X LINKED ICHTHYOSIS;

CHOLESTEROL SULFATE; CORNEODESMOSOMES; EPIDERMAL BARRIER FUNCTION; EPIDERMAL LIPID METABOLISM; STEROID SULFATASE; X-LINKED ICHTHYOSIS;

CELL DIFFERENTIATION; CHOLESTEROL ESTERS; EPIDERMIS; FEMALE; HUMANS; ICHTHYOSIS, X-LINKED; MALE; SULFOTRANSFERASES;

EID: 84896713353     PISSN: 13881981     EISSN: 18792618     Source Type: Journal    
DOI: 10.1016/j.bbalip.2013.11.009     Document Type: Review

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