Loss of AMP-activated protein kinase in X-linked adrenoleukodystrophy patient-derived fibroblasts and lymphocytes

Biochemical and Biophysical Research Communications

Volumn 445, Issue 1, 2014, Pages 126-131

  Singh, Jaspreet ^a   Giri, Shailendra ^a  

^a HENRY FORD HEALTH SYSTEM   (United States)

Author keywords

AMPK 1; ECAR; Inflammation; OCR; Ubiquitin; X ALD

Indexed keywords

HYDROXYMETHYLGLUTARYL COENZYME A REDUCTASE KINASE; HYDROXYMETHYLGLUTARYL COENZYME A REDUCTASE KINASE ALPHA1; MESSENGER RNA; UNCLASSIFIED DRUG;

ACIDIFICATION; ADRENOLEUKODYSTROPHY; ARTICLE; CHILDHOOD ADRENOLEUKODYSTROPHY; CONTROLLED STUDY; DISEASE SEVERITY; DISORDERS OF PEROXISOMAL FUNCTIONS; FIBROBLAST; GENE EXPRESSION; GENE MUTATION; GENETIC VARIABILITY; HUMAN; HUMAN CELL; LYMPHOCYTE; OXYGEN CONSUMPTION; PHENOTYPE; PRIORITY JOURNAL; PROTEIN DEPLETION; UBIQUITINATION;

AMPKΑ1; ECAR; INFLAMMATION; OCR; UBIQUITIN; X-ALD;

ADRENOLEUKODYSTROPHY; AMP-ACTIVATED PROTEIN KINASES; CELLS, CULTURED; CYTOKINES; DOWN-REGULATION; FEMALE; FIBROBLASTS; GENE EXPRESSION; HUMANS; IMMUNOBLOTTING; LYMPHOCYTES; MITOCHONDRIA; NITRIC OXIDE SYNTHASE TYPE II; OXYGEN CONSUMPTION; REVERSE TRANSCRIPTASE POLYMERASE CHAIN REACTION; UBIQUITIN;

EID: 84896698571     PISSN: 0006291X     EISSN: 10902104     Source Type: Journal    
DOI: 10.1016/j.bbrc.2014.01.126     Document Type: Article

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