Ribosomal protein deficiency causes Tp53-independent erythropoiesis failure in zebrafish

International Journal of Biochemistry and Cell Biology

Volumn 49, Issue 1, 2014, Pages 1-7

  Yadav, Gnaneshwar V ^a   Chakraborty, Anirban ^a,b   Uechi, Tamayo ^a   Kenmochi, Naoya ^a  

^a UNIVERSITY OF MIYAZAKI   (Japan)

^b UNIVERSITÉ DE TOULOUSE   (France)

Author keywords

DBA; Ribosomal proteins; Ribosomopathy; Tp53; Zebrafish

Indexed keywords

ARGININE; LEUCINE; MAMMALIAN TARGET OF RAPAMYCIN COMPLEX 1; MESSENGER RNA; PROTEIN P53; RAPAMYCIN; RIBOSOME PROTEIN; ZEBRAFISH PROTEIN;

ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; BLACKFAN DIAMOND ANEMIA; CELL MATURATION; CELL PROLIFERATION; CELL STRUCTURE; CIRCULATION; CONTROLLED STUDY; ENZYME ACTIVATION; ERYTHROCYTE COUNT; ERYTHROID CELL; ERYTHROPOIESIS; GENE SILENCING; LOSS OF FUNCTION MUTATION; NONHUMAN; PHENOTYPE; PROTEIN DEFECT; PROTEIN FUNCTION; PURE RED CELL ANEMIA; RIBOSOMAL PROTEIN DEFICIENCY; RNA TRANSLATION; SIGNAL TRANSDUCTION; ANIMAL; ANIMAL EMBRYO; DEFICIENCY; DRUG EFFECTS; EMBRYOLOGY; GENE EXPRESSION REGULATION; GENETICS; HUMAN; METABOLISM; REVERSE TRANSCRIPTION POLYMERASE CHAIN REACTION; RIBOSOME; ZEBRA FISH;

ANEMIA, DIAMOND-BLACKFAN; ANIMALS; ARGININE; EMBRYO, NONMAMMALIAN; ERYTHROCYTE COUNT; ERYTHROID CELLS; ERYTHROPOIESIS; GENE EXPRESSION REGULATION, DEVELOPMENTAL; GENE KNOCKDOWN TECHNIQUES; HUMANS; LEUCINE; REVERSE TRANSCRIPTASE POLYMERASE CHAIN REACTION; RIBOSOMAL PROTEINS; RIBOSOMES; SIROLIMUS; TUMOR SUPPRESSOR PROTEIN P53; ZEBRAFISH; ZEBRAFISH PROTEINS;

EID: 84893170360     PISSN: 13572725     EISSN: 18785875     Source Type: Journal    
DOI: 10.1016/j.biocel.2014.01.006     Document Type: Article

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