Pathogenesis of the erythroid failure in Diamond Blackfan anaemia

British Journal of Haematology

Volumn 148, Issue 4, 2010, Pages 611-622

  Sieff, Colin A ^a,b   Yang, Jing ^a,b   Merida Long, Lilia B ^a   Lodish, Harvey F ^a  

^a WHITEHEAD INSTITUTE FOR BIOMEDICAL RESEARCH   (United States)

^b BOSTON CHILDREN S HOSPITAL   (United States)

Author keywords

Diamond Blackfan anaemia; Erythropoiesis; Nucleolar stress; Red cell aplasia; RPS19

Indexed keywords

MESSENGER RNA; PROTEIN MYB; PROTEIN P21; PROTEIN P53; RIBOSOME PROTEIN; SHORT HAIRPIN RNA; SMALL INTERFERING RNA; STEM CELL FACTOR;

ANIMAL CELL; ARTICLE; BLACKFAN DIAMOND ANEMIA; CELL COUNT; CELL CYCLE ARREST; CELL CYCLE G1 PHASE; CELL CYCLE S PHASE; CELL DIFFERENTIATION; CELL MATURATION; CELL PROLIFERATION; CELL SURFACE; CONTROLLED STUDY; ENUCLEATION; ERYTHROID CELL; ERYTHROID PRECURSOR CELL; ERYTHROPOIESIS; MOUSE; NONHUMAN; PATHOGENESIS; PRIORITY JOURNAL; PROTEIN DEPLETION; RNA SYNTHESIS;

ANEMIA, DIAMOND-BLACKFAN; CELL DIFFERENTIATION; CELL PROLIFERATION; CELLS, CULTURED; ERYTHROPOIESIS; G1 PHASE; GENE KNOCKDOWN TECHNIQUES; GENES, MYB; HUMANS; LIVER; REVERSE TRANSCRIPTASE POLYMERASE CHAIN REACTION; RIBOSOMAL PROTEINS; RNA; RNA, SMALL INTERFERING; TUMOR SUPPRESSOR PROTEIN P53;

EID: 75149195242     PISSN: 00071048     EISSN: 13652141     Source Type: Journal    
DOI: 10.1111/j.1365-2141.2009.07993.x     Document Type: Article

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