Mineral particle size in children with osteogenesis imperfecta type I is not increased independently of specific collagen mutations

Bone

Volumn 60, Issue , 2014, Pages 122-1128

  Fratzl Zelman, Nadja ^a   Schmidt, Ingo ^b   Roschger, Paul ^a   Glorieux, Francis H ^c   Klaushofer, Klaus ^a   Fratzl, Peter ^b   Rauch, Frank ^c   Wagermaier, Wolfgang ^b  

^a LUDWIG BOLTZMANN INSTITUTE FOR LUNG VASCULAR RESEARCH   (Austria)

^b MAX PLANCK INSTITUTE OF COLLOIDS AND INTERFACES   (Germany)

^c SHRINERS HOSPITAL FOR CHILDREN   (Canada)

Author keywords

Bone biopsies; Haploinsufficiency and structural mutations; Mineral particle size; Osteogenesis imperfecta; Quantitative backscattered electron microscopy; Synchrotron small angle X ray scattering

Indexed keywords

CALCIUM; COLLAGEN TYPE 1; COLLAGEN; MINERAL; NANOMATERIAL;

ARTICLE; BONE BIOPSY; BONE MATRIX; BONE MINERAL; BONE MINERALIZATION; CHILD; CLINICAL ARTICLE; CONTROLLED STUDY; FEMALE; GENE MUTATION; GENOTYPE; HUMAN; HUMAN CELL; HUMAN TISSUE; LINEAR REGRESSION ANALYSIS; MALE; OSTEOGENESIS IMPERFECTA; OSTEOGENESIS IMPERFECTA TYPE I; PARTICLE SIZE; PRESCHOOL CHILD; QUALITATIVE ANALYSIS; QUANTITATIVE ANALYSIS; RADIATION BEAM; RADIATION SCATTERING; SCHOOL CHILD; SYNCHROTRON RADIATION; TRABECULAR BONE; X RAY DIFFRACTION; BONE BIOPSIES; CASE CONTROL STUDY; CHEMISTRY; GENETICS; HAPLOINSUFFICIENCY AND STRUCTURAL MUTATIONS; MINERAL PARTICLE SIZE; MUTATION; PATHOLOGY; QUANTITATIVE BACKSCATTERED ELECTRON MICROSCOPY; SMALL ANGLE SCATTERING; SYNCHROTRON SMALL ANGLE X-RAY SCATTERING;

BONE BIOPSIES; HAPLOINSUFFICIENCY AND STRUCTURAL MUTATIONS; MINERAL PARTICLE SIZE; OSTEOGENESIS IMPERFECTA; QUANTITATIVE BACKSCATTERED ELECTRON MICROSCOPY; SYNCHROTRON SMALL ANGLE X-RAY SCATTERING;

CASE-CONTROL STUDIES; CHILD; CHILD, PRESCHOOL; COLLAGEN; FEMALE; HUMANS; MALE; MINERALS; MUTATION; NANOSTRUCTURES; OSTEOGENESIS IMPERFECTA; PARTICLE SIZE; SCATTERING, SMALL ANGLE; X-RAY DIFFRACTION;

EID: 84891140691     PISSN: 87563282     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.bone.2013.11.023     Document Type: Article

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