Laminin β2 gene missense mutation produces endoplasmic reticulum stress in podocytes

Journal of the American Society of Nephrology

Volumn 24, Issue 8, 2013, Pages 1223-1233

  Chen, Ying Maggie ^a   Zhou, Yuefang ^a   Go, Gloriosa ^a   Marmerstein, Joseph T ^a   Kikkawa, Yamato ^b   Miner, Jeffrey H ^a  

^a WASHINGTON UNIVERSITY SCHOOL OF MEDICINE   (United States)

^b TOKYO UNIVERSITY OF PHARMACY AND LIFE SCIENCES   (Japan)

Author keywords

[No Author keywords available]

Indexed keywords

CCAAT ENHANCER BINDING PROTEIN; CCAAT ENHANCER BINDING PROTEIN HOMOLOGOUS PROTEIN; LAMININ; LAMININ ALPHA1; LAMININ ALPHA2; LAMININ BETA1; LAMININ BETA2; MUTANT PROTEIN; TAURODEOXYCHOLIC ACID; UNCLASSIFIED DRUG;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; APOPTOSIS; ARTICLE; CELL DAMAGE; CELL ULTRASTRUCTURE; CONFOCAL MICROSCOPY; CONGENITAL NEPHROTIC SYNDROME; CONTROLLED STUDY; DISEASE SEVERITY; ENDOPLASMIC RETICULUM STRESS; GENE; GENE EXPRESSION; GLOMERULUS BASEMENT MEMBRANE; IMMUNOFLUORESCENCE MICROSCOPY; IN SITU HYBRIDIZATION; KIDNEY FAILURE; LAMININ BETA2 GENE; MICROSCOPY; MISSENSE MUTATION; MOUSE; NONHUMAN; PERINATAL PERIOD; PIERSON SYNDROME; PODOCYTE; PRIORITY JOURNAL; PROTEIN FOLDING; PROTEIN SECRETION; PROTEINURIA; TRANSGENE; TRANSGENIC MOUSE; TRANSMISSION ELECTRON MICROSCOPY;

EID: 84881093680     PISSN: 10466673     EISSN: 15333450     Source Type: Journal    
DOI: 10.1681/ASN.2012121149     Document Type: Article

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