Subcellular localization of dystrophin isoforms in cardiomyocytes and Phenotypic analysis of dystrophin-deficient mice Reveal cardiac myopathy is predominantly caused by a deficiency in full-length dystrophin

Experimental Animals

Volumn 62, Issue 3, 2013, Pages 211-217

  Masubuchi, Nami ^a   Shidoh, Yuichi ^a   Kondo, Shunzo ^b   Takatoh, Jun ^c   Hanaoka, Kazunori ^a  

^a KITASATO UNIVERSITY   (Japan)

^b JEOL LTD   (Japan)

^c DUKE UNIVERSITY MEDICAL CENTER   (United States)

Author keywords

Cardiomyopathy; dp427; dp71; Dystrophin; Heart

Indexed keywords

DYSTROPHIN; DYSTROPHIN 427; DYSTROPHIN 71; ISOPROTEIN; UNCLASSIFIED DRUG;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CARDIOMYOPATHY; CELLULAR DISTRIBUTION; CONTROLLED STUDY; DENSITY GRADIENT CENTRIFUGATION; DISEASE SEVERITY; GENETIC ASSOCIATION; HEART MUSCLE CELL; HEART MUSCLE FIBER MEMBRANE; HEART MUSCLE FIBROSIS; HEART MUSCLE NECROSIS; HISTOPATHOLOGY; MOUSE; NONHUMAN; PHENOTYPE; PROTEIN DEFICIENCY; PROTEIN DEPLETION; PROTEIN EXPRESSION; PROTEIN FUNCTION; PROTEIN LOCALIZATION; TRANSVERSE TUBULAR SYSTEM; ANIMAL; C57BL MOUSE; CBA MOUSE; CYTOLOGY; DEFICIENCY; FIBROSIS; GENETICS; HEART MUSCLE; INBRED MOUSE STRAIN; METABOLISM; PATHOLOGY; SARCOLEMMA;

ANIMALS; CARDIOMYOPATHIES; DYSTROPHIN; FIBROSIS; MICE; MICE, INBRED C57BL; MICE, INBRED CBA; MICE, INBRED STRAINS; MYOCARDIUM; MYOCYTES, CARDIAC; PHENOTYPE; PROTEIN ISOFORMS; SARCOLEMMA;

EID: 84880970348     PISSN: 13411357     EISSN: None     Source Type: Journal    
DOI: 10.1538/expanim.62.211     Document Type: Article

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