Intracellularly-retained decorin lacking the C-terminal ear repeat causes ER stress: A cell-based etiological mechanism for congenital stromal corneal dystrophy

American Journal of Pathology

Volumn 183, Issue 1, 2013, Pages 247-256

  Chen, Shoujun ^a   Sun, Mei ^a   Iozzo, Renato V ^b   Kao, Winston W Y ^c   Birk, David E ^a  

^a UNIVERSITY OF SOUTH FLORIDA   (United States)

^b THOMAS JEFFERSON UNIVERSITY   (United States)

^c UNIVERSITY OF CINCINNATI COLLEGE OF MEDICINE   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

DECORIN;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; CARBOXY TERMINAL SEQUENCE; CELL STRUCTURE; CELLULAR DISTRIBUTION; CONGENITAL CORNEA DYSTROPHY; CONGENITAL STROMAL CORNEAL DYSTROPHY; CONTROLLED STUDY; CORNEA CELL; CORNEA OPACITY; CYTOPLASM; EMBRYO CELL; ENDOPLASMIC RETICULUM STRESS; GOLGI COMPLEX; HUMAN; HUMAN CELL; IN VIVO STUDY; KIDNEY CELL; MOUSE; NONHUMAN; PATHOPHYSIOLOGY; PRIORITY JOURNAL; PROTEIN EXPRESSION; PROTEIN LOCALIZATION; PROTEIN SECRETION; PROTEIN SYNTHESIS; UNFOLDED PROTEIN RESPONSE;

ANIMALS; CORNEAL DYSTROPHIES, HEREDITARY; DECORIN; ENDOPLASMIC RETICULUM; FLUORESCENT ANTIBODY TECHNIQUE; GENETIC MARKERS; HEK293 CELLS; HUMANS; IMMUNOBLOTTING; MICE; MICE, TRANSGENIC; MICROSCOPY, CONFOCAL; MICROSCOPY, ELECTRON, TRANSMISSION; POINT MUTATION; POLYMERASE CHAIN REACTION; PROTEIN TRANSPORT; STRESS, PHYSIOLOGICAL; TERMINAL REPEAT SEQUENCES;

EID: 84879368222     PISSN: 00029440     EISSN: 15252191     Source Type: Journal    
DOI: 10.1016/j.ajpath.2013.04.001     Document Type: Article

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