Pathophysiological mechanisms of autosomal dominant congenital stromal corneal dystrophy: C-terminaltruncated decorin results in abnormal matrix assembly and altered expression of small leucine-rich proteoglycans

American Journal of Pathology

Volumn 179, Issue 5, 2011, Pages 2409-2419

  Chen, Shoujun ^a   Sun, Mei ^a   Meng, Xianmin ^a   Iozzo, Renato V ^b   Kao, Winston W Y ^c   Birk, David E ^a  

^a UNIVERSITY OF SOUTH FLORIDA   (United States)

^b THOMAS JEFFERSON UNIVERSITY   (United States)

^c UNIVERSITY OF CINCINNATI COLLEGE OF MEDICINE   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

BIGLYCAN; DECORIN; FIBROMODULIN; KERATOCAN; LUMICAN;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; AUTOSOMAL DOMINANT DISORDER; CARBOXY TERMINAL SEQUENCE; CONGENITAL CORNEA DYSTROPHY; CONTROLLED STUDY; CORNEA CELL; CORNEA OPACITY; DISEASE SEVERITY; EXTRACELLULAR MATRIX; FRAMESHIFT MUTATION; LAMELLAR BODY; MOUSE; NONHUMAN; PRIORITY JOURNAL; PROTEIN EXPRESSION; STROMA; TRANSGENIC MOUSE; WILD TYPE;

ANIMALS; CORNEAL DYSTROPHIES, HEREDITARY; CORNEAL OPACITY; DECORIN; DISEASE MODELS, ANIMAL; EXTRACELLULAR MATRIX; FIBRILLAR COLLAGENS; FRAMESHIFT MUTATION; HETEROZYGOTE; MICE; MICE, TRANSGENIC;

EID: 80055005154     PISSN: 00029440     EISSN: 15252191     Source Type: Journal    
DOI: 10.1016/j.ajpath.2011.07.026     Document Type: Article

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