The distribution and functional properties of Pelizaeus-Merzbacher-like disease-linked Cx47 mutations on Cx47/Cx47 homotypic and Cx47/Cx43 heterotypic gap junctions

Biochemical Journal

Volumn 452, Issue 2, 2013, Pages 249-258

  Kim, Mi Seong ^a   Gloor, Gregory B ^a   Bai, Donglin ^a  

^a UNIVERSITY OF WESTERN ONTARIO   (Canada)

Author keywords

Connexin47; Gap junction; Hypomyelination; Pelizaeus Merzbacher like disease

Indexed keywords

CONNEXIN 43; CONNEXIN 47;

5' UNTRANSLATED REGION; AMINO ACID SEQUENCE; ARTICLE; ASTROCYTE; CELL JUNCTION; CELLULAR DISTRIBUTION; CENTRAL NERVOUS SYSTEM; GAP JUNCTION; GENE EXPRESSION; HELA CELL; HUMAN; MUTATION; NUCLEOTIDE SEQUENCE; OLIGODENDROGLIA; PRIORITY JOURNAL; START CODON; STEADY STATE;

AMINO ACID SEQUENCE; AMINO ACID SUBSTITUTION; BASE SEQUENCE; CONNEXIN 43; CONNEXINS; GAP JUNCTIONS; HELA CELLS; HUMANS; MOLECULAR SEQUENCE DATA; MUTANT PROTEINS; NEUROGLIA; PELIZAEUS-MERZBACHER DISEASE; RECOMBINANT FUSION PROTEINS; SEQUENCE HOMOLOGY, AMINO ACID;

EID: 84877726260     PISSN: 02646021     EISSN: 14708728     Source Type: Journal    
DOI: 10.1042/BJ20121821     Document Type: Article

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