-
1
-
-
34948886661
-
Progressive oxidative damage in the central nervous system of a murine model for juvenile Batten disease
-
J.W. Benedict, C.A. Sommers, and D.A. Pearce Progressive oxidative damage in the central nervous system of a murine model for juvenile Batten disease J. Neurosci. Res. 85 2007 2882 2891
-
(2007)
J. Neurosci. Res.
, vol.85
, pp. 2882-2891
-
-
Benedict, J.W.1
Sommers, C.A.2
Pearce, D.A.3
-
3
-
-
76049083966
-
Reactive oxygen species, cellular redox systems, and apoptosis
-
M.L. Circu, and T.Y. Aw Reactive oxygen species, cellular redox systems, and apoptosis Free Radic. Biol. Med. 48 2010 749 762
-
(2010)
Free Radic. Biol. Med.
, vol.48
, pp. 749-762
-
-
Circu, M.L.1
Aw, T.Y.2
-
4
-
-
0029147298
-
Isolation of a novel gene underlying Batten disease, CLN3
-
The International Batten Disease Consortium
-
The International Batten Disease Consortium Isolation of a novel gene underlying Batten disease, CLN3 Cell 82 1995 949 957
-
(1995)
Cell
, vol.82
, pp. 949-957
-
-
-
5
-
-
0030863670
-
Requirement for GD3 ganglioside in CD95- and ceramide-induced apoptosis
-
R. De Maria Requirement for GD3 ganglioside in CD95- and ceramide-induced apoptosis Science 277 1997 1652 1655
-
(1997)
Science
, vol.277
, pp. 1652-1655
-
-
De Maria, R.1
-
6
-
-
33749007392
-
Oxidative stress induces phosphoenolpyruvate carboxykinase expression in H4IIE cells
-
Y. Ito, S. Oumi, T. Nagasawa, and N. Nishizawa Oxidative stress induces phosphoenolpyruvate carboxykinase expression in H4IIE cells Biosci. Biotechnol. Biochem. 70 2006 2191 2198
-
(2006)
Biosci. Biotechnol. Biochem.
, vol.70
, pp. 2191-2198
-
-
Ito, Y.1
Oumi, S.2
Nagasawa, T.3
Nishizawa, N.4
-
7
-
-
58849160520
-
Ceramide and neurodegeneration: Susceptibility of neurons and oligodendrocytes to cell damage and death
-
A. Jana, E.L. Hogan, and K. Pahan Ceramide and neurodegeneration: susceptibility of neurons and oligodendrocytes to cell damage and death J. Neurol. Sci. 278 2009 5 15
-
(2009)
J. Neurol. Sci.
, vol.278
, pp. 5-15
-
-
Jana, A.1
Hogan, E.L.2
Pahan, K.3
-
8
-
-
77954143409
-
Omega-3 and omega-6 fatty acids suppress ER- and oxidative stress in cultured neurons and neuronal progenitor cells from mice lacking PPT1
-
S.-J. Kim, Z. Zhang, A. Saha, C. Sarkar, Z. Zhao, Y. Xu, and A.B. Mukherjee Omega-3 and omega-6 fatty acids suppress ER- and oxidative stress in cultured neurons and neuronal progenitor cells from mice lacking PPT1 Neurosci. Lett. 479 2010 292 296
-
(2010)
Neurosci. Lett.
, vol.479
, pp. 292-296
-
-
Kim, S.-J.1
Zhang, Z.2
Saha, A.3
Sarkar, C.4
Zhao, Z.5
Xu, Y.6
Mukherjee, A.B.7
-
9
-
-
0031919157
-
Regulation of ceramide production and apoptosis
-
R.N. Kolesnick, and M. Krönke Regulation of ceramide production and apoptosis Annu. Rev. Physiol. 60 1998 643 665
-
(1998)
Annu. Rev. Physiol.
, vol.60
, pp. 643-665
-
-
Kolesnick, R.N.1
Krönke, M.2
-
10
-
-
0037122008
-
Acetylation suppresses the proapoptotic activity of GD3 ganglioside
-
F. Malisan, L. Franchi, B. Tomassini, N. Ventura, I. Condo, M.R. Rippo, A. Rufini, L. Liberati, C. Nachtigall, B. Kniep, and R. Testi Acetylation suppresses the proapoptotic activity of GD3 ganglioside J. Exp. Med. 196 2002 1535 1541
-
(2002)
J. Exp. Med.
, vol.196
, pp. 1535-1541
-
-
Malisan, F.1
Franchi, L.2
Tomassini, B.3
Ventura, N.4
Condo, I.5
Rippo, M.R.6
Rufini, A.7
Liberati, L.8
Nachtigall, C.9
Kniep, B.10
Testi, R.11
-
11
-
-
58249093939
-
How mitochondria produce reactive oxygen species
-
M.P. Murphy How mitochondria produce reactive oxygen species Biochem. J. 417 2009 1
-
(2009)
Biochem. J.
, vol.417
, pp. 1
-
-
Murphy, M.P.1
-
12
-
-
34347398122
-
Nitric oxide signaling is disrupted in the yeast model for Batten disease
-
N.S. Osório, A. Carvalho, A.J. Almeida, S. Padilla-Lopez, C. Leão, J. Laranjinha, P. Ludovico, D.A. Pearce, and F. Rodrigues Nitric oxide signaling is disrupted in the yeast model for Batten disease Mol. Biol. Cell 18 2007 2755 2767
-
(2007)
Mol. Biol. Cell
, vol.18
, pp. 2755-2767
-
-
Osório, N.S.1
Carvalho, A.2
Almeida, A.J.3
Padilla-Lopez, S.4
Leão, C.5
Laranjinha, J.6
Ludovico, P.7
Pearce, D.A.8
Rodrigues, F.9
-
13
-
-
0030833658
-
Upregulation of Bcl-2 and elevation of ceramide in Batten disease
-
K. Puranam, W.H. Qian, K. Nikbakht, M. Venable, L. Obeid, Y. Hannun, and R.M. Boustany Upregulation of Bcl-2 and elevation of ceramide in Batten disease Neuropediatrics 28 2007 37 41
-
(2007)
Neuropediatrics
, vol.28
, pp. 37-41
-
-
Puranam, K.1
Qian, W.H.2
Nikbakht, K.3
Venable, M.4
Obeid, L.5
Hannun, Y.6
Boustany, R.M.7
-
14
-
-
0033810454
-
GD3 ganglioside directly targets mitochondria in a bcl-2-controlled fashion
-
M.R. Rippo, F. Malisan, L. Ravagnan, B. Tomassini, I. Condo, P. Costantini, S.A. Susin, A. Rufini, M. Todaro, G. Kroemer, and R. Testi GD3 ganglioside directly targets mitochondria in a bcl-2-controlled fashion FASEB J. 14 2000 2047 2054
-
(2000)
FASEB J.
, vol.14
, pp. 2047-2054
-
-
Rippo, M.R.1
Malisan, F.2
Ravagnan, L.3
Tomassini, B.4
Condo, I.5
Costantini, P.6
Susin, S.A.7
Rufini, A.8
Todaro, M.9
Kroemer, G.10
Testi, R.11
-
15
-
-
84860889760
-
The pyruvate dehydrogenase complex as a therapeutic target for age-related diseases
-
P.W. Stacpoole The pyruvate dehydrogenase complex as a therapeutic target for age-related diseases Aging Cell 11 2012 371 377
-
(2012)
Aging Cell
, vol.11
, pp. 371-377
-
-
Stacpoole, P.W.1
-
16
-
-
57649233079
-
The role of mitochondria in reactive oxygen species metabolism and signaling
-
A. Starkov The role of mitochondria in reactive oxygen species metabolism and signaling Ann. NY Acad. Sci. 1147 2008 37 52
-
(2008)
Ann. NY Acad. Sci.
, vol.1147
, pp. 37-52
-
-
Starkov, A.1
-
17
-
-
79955381027
-
The Batten disease gene CLN3 is required for the response to oxidative stress
-
R.I. Tuxworth, H. Chen, V. Vivancos, N. Carvajal, X. Huang, and G. Tear The Batten disease gene CLN3 is required for the response to oxidative stress Hum. Mol. Gen. 20 2011 2037 2047
-
(2011)
Hum. Mol. Gen.
, vol.20
, pp. 2037-2047
-
-
Tuxworth, R.I.1
Chen, H.2
Vivancos, V.3
Carvajal, N.4
Huang, X.5
Tear, G.6
-
18
-
-
0030993576
-
Sialic acids as ligands in recognition phenomena
-
A. Varki Sialic acids as ligands in recognition phenomena FASEB J. 11 1997 248 255
-
(1997)
FASEB J.
, vol.11
, pp. 248-255
-
-
Varki, A.1
-
20
-
-
0014618774
-
Tricarballylate and hydroxycitrate: Substrate and inhibitor of ATP: Citrate oxaloacetate lyase
-
J.A. Watson, M. Fang, and J.M. Lowenstein Tricarballylate and hydroxycitrate: substrate and inhibitor of ATP: citrate oxaloacetate lyase Arch. Biochem. Biophys. 135 1969 209 217
-
(1969)
Arch. Biochem. Biophys.
, vol.135
, pp. 209-217
-
-
Watson, J.A.1
Fang, M.2
Lowenstein, J.M.3
-
21
-
-
80054064688
-
Protective potential of resveratrol against oxidative stress and apoptosis in Batten disease lymphoblast cells
-
D.-H. Yoon, O.-Y. Kwon, J.Y. Mang, M.J. Jung, Do.Yeon. Kim, Y.K. Park, T.-H. Heo, and S.-J. Kim Protective potential of resveratrol against oxidative stress and apoptosis in Batten disease lymphoblast cells Biochem. Biophys. Res. Commun. 414 2011 49 52
-
(2011)
Biochem. Biophys. Res. Commun.
, vol.414
, pp. 49-52
-
-
Yoon, D.-H.1
Kwon, O.-Y.2
Mang, J.Y.3
Jung, M.J.4
Kim, Do.Yeon.5
Park, Y.K.6
Heo, T.-H.7
Kim, S.-J.8
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