Electrodiagnostic testing and histopathologic changes confirm peripheral nervous system myelin abnormalities in the feline model of niemann-pick disease type C

Journal of Neuropathology and Experimental Neurology

Volumn 72, Issue 3, 2013, Pages 256-262

  Bagel, Jessica H ^a   Sikora, Tracey U ^a   Prociuk, Maria ^a   Pesayco, Jill P ^b   Mizisin, Andrew P ^b   Shelton, G Diane ^b   Vite, Charles H ^a  

^a UNIVERSITY OF PENNSYLVANIA   (United States)

^b UNIVERSITY OF CALIFORNIA   (United States)

Author keywords

Animal model; Feline; Lysosomal storage disease; Neuropathy; Niemann Pick type C; Peripheral nerve.

Indexed keywords

MYELIN;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CAT; CELL VACUOLE; CONTROLLED STUDY; ELECTRODIAGNOSIS; ELECTROMYOGRAPH; ELECTROMYOGRAPHY; ELECTRON MICROSCOPY; HISTOPATHOLOGY; MISSENSE MUTATION; MOTOR NERVE CONDUCTION; MUSCLE ACTION POTENTIAL; MYELIN DEFICIENCY; MYELIN SHEATH; MYELINATED NERVE; NERVE FIBER DEGENERATION; NEUROPATHOLOGY; NIEMANN PICK DISEASE; NONHUMAN; PERIPHERAL NERVE; PRIORITY JOURNAL; SCHWANN CELL; SENSORY NERVE CONDUCTION;

ANIMALS; CATS; DISEASE MODELS, ANIMAL; ELECTROPHYSIOLOGY; MICROSCOPY, ELECTRON, TRANSMISSION; MYELIN SHEATH; NIEMANN-PICK DISEASE, TYPE C; ULNAR NERVE;

EID: 84874648594     PISSN: 00223069     EISSN: 15546578     Source Type: Journal    
DOI: 10.1097/NEN.0b013e318286587f     Document Type: Article

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