Apical CFTR Expression in Human Nasal Epithelium Correlates with Lung Disease in Cystic Fibrosis

PLoS ONE

Volumn 8, Issue 3, 2013, Pages

  van Meegen, Marit Arianne ^a   Terheggen Lagro, Suzanne Willemina Julia ^a   Koymans, Kirsten Judith ^a   van der Ent, Cornelis Korstiaan ^a   Beekman, Jeffrey Matthijn ^a  

^a UNIVERSITY MEDICAL CENTER UTRECHT   (Netherlands)

Author keywords

[No Author keywords available]

Indexed keywords

CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR; EZRIN; UVOMORULIN;

APICAL MEMBRANE; ARTICLE; CELL DIFFERENTIATION; CELL POPULATION; CONFOCAL MICROSCOPY; CONTROLLED STUDY; CORRELATION ANALYSIS; CORRELATION COEFFICIENT; DISEASE SEVERITY; FORCED EXPIRATORY VOLUME; FRAMESHIFT MUTATION; HOMOZYGOSITY; HUMAN; HUMAN CELL; IMMUNOLOCALIZATION; LUNG DISEASE; LUNG FIBROSIS; LUNG FUNCTION; MISSENSE MUTATION; MORPHOLOGY; NONSENSE MUTATION; NOSE MUCOSA; PROTEIN EXPRESSION; PROTEIN LOCALIZATION; QUANTITATIVE ANALYSIS;

ADOLESCENT; CASE-CONTROL STUDIES; CELL POLARITY; CHILD; CYSTIC FIBROSIS; CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR; EPITHELIAL CELLS; FEMALE; HUMANS; MALE; MICROSCOPY, CONFOCAL; MUTATION; NASAL MUCOSA; PROTEIN TRANSPORT; REPRODUCIBILITY OF RESULTS; RESPIRATORY FUNCTION TESTS;

EID: 84874614232     PISSN: None     EISSN: 19326203     Source Type: Journal    
DOI: 10.1371/journal.pone.0057617     Document Type: Article

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