Ten patient stories illustrating the extraordinarily diverse clinical features of patients with thrombotic thrombocytopenic purpura and severe ADAMTS13 deficiency

Journal of Clinical Apheresis

Volumn 27, Issue 6, 2012, Pages 302-311

  George, James N ^a   Chen, Qiaofang ^a   Deford, Cassie C ^a   Al Nouri, Zayd ^a  

^a UNIVERSITY OF OKLAHOMA HEALTH SCIENCES CENTER   (United States)

Author keywords

bacterial endocarditis; microangiopathic hemolytic anemia; systemic lupus erythematosus; thrombocytopenia; Upshaw Schulman syndrome

Indexed keywords

AUTOANTIBODY; AZATHIOPRINE; BILIRUBIN; CORTICOSTEROID; CREATININE; LACTATE DEHYDROGENASE; PREDNISONE; RITUXIMAB; TROPONIN; VON WILLEBRAND FACTOR CLEAVING PROTEINASE;

ABDOMINAL DISCOMFORT; ABDOMINAL PAIN; ABDOMINAL TENDERNESS; ADAMTS13 DEFICIENCY; ADULT; ANEMIA; AORTA VALVE REPLACEMENT; ARTICLE; ATAXIC APHASIA; AUTOIMMUNE DISEASE; BACTERIAL ENDOCARDITIS; BLOOD SMEAR; BLOODY DIARRHEA; BRAIN EDEMA; CHILD; CLINICAL ARTICLE; CLINICAL FEATURE; CORTICOSTEROID THERAPY; DIARRHEA; DISEASE COURSE; DYSARTHRIA; DYSPNEA; ECHOCARDIOGRAPHY; ELLIPTOCYTOSIS; EPIGASTRIC PAIN; FAINTNESS; FAMILIAL DISEASE; FATIGUE; FECES CULTURE; FEMALE; GENETIC DISORDER; HEADACHE; HEART LEFT VENTRICLE HYPERTROPHY; HEART VENTRICLE TACHYCARDIA; HEMATOCRIT; HEMATURIA; HUMAN; HYPOXEMIA; IMMUNOBLOTTING; JAUNDICE; MALE; MALIGNANT HYPERTENSION; MEDICAL HISTORY; MENORRHAGIA; NAUSEA; NON ST SEGMENT ELEVATION MYOCARDIAL INFARCTION; PARESTHESIA; PHYSICAL EXAMINATION; PLASMAPHERESIS; PROTEIN DEFICIENCY; PROTEINURIA; SCHOOL CHILD; ST SEGMENT ELEVATION MYOCARDIAL INFARCTION; SWELLING; SYSTEMIC LUPUS ERYTHEMATOSUS; THORAX PAIN; THROMBOCYTE COUNT; THROMBOCYTOPENIA; THROMBOSIS; THROMBOTIC THROMBOCYTOPENIC PURPURA; URINALYSIS; UTERUS MYOMA; VOMITING; WEAKNESS;

ADAM PROTEINS; ADULT; AUTOANTIBODIES; AUTOANTIGENS; CHILD; DIAGNOSIS, DIFFERENTIAL; DIAGNOSTIC ERRORS; ELLIPTOCYTOSIS, HEREDITARY; ENDOCARDITIS, BACTERIAL; FEMALE; FOODBORNE DISEASES; HEMOLYTIC-UREMIC SYNDROME; HUMANS; HYPERTENSION; INDIVIDUALITY; LUPUS ERYTHEMATOSUS, SYSTEMIC; MALE; MENINGITIS, BACTERIAL; MIDDLE AGED; PHENOTYPE; PURPURA, THROMBOTIC THROMBOCYTOPENIC; RECURRENCE; STAPHYLOCOCCAL INFECTIONS; STROKE; YOUNG ADULT;

EID: 84870902189     PISSN: 07332459     EISSN: 10981101     Source Type: Journal    
DOI: 10.1002/jca.21248     Document Type: Article

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