Pregnancy-induced thrombocytopenia and TTP, and the risk of fetal death, in Upshaw-Schulman syndrome: A series of 15 pregnancies in 9 genotyped patients

British Journal of Haematology

Volumn 144, Issue 5, 2009, Pages 742-754

  Fujimura, Yoshihiro ^a   Matsumoto, Masanori ^a   Kokame, Koichi ^b   Isonishi, Ayami ^a   Soejima, Kenji ^c   Akiyama, Nobu ^d   Tomiyama, Junji ^d   Natori, Kazuhiko ^e   Kuranishi, Yasunobu ^e   Imamura, Yutaka ^f   Inoue, Nobumasa ^g   Higasa, Satoshi ^h   Seike, Masako ⁱ   Kozuka, Teruhiko ⁱ   Hara, Masamichi ⁱ   Wada, Hideo ^j   Murata, Mitsuru ^k   Ikeda, Yasuo ^k   Miyata, Toshiyuki ^b   George, James N ^l  

^a NARA MEDICAL UNIVERSITY   (Japan)

^b NATIONAL CEREBRAL AND CARDIOVASCULAR CENTER   (Japan)

^c Chemo Sero Therapeutic Research Institute   (Japan)

^d TOKYO METROPOLITAN BOKUTOH HOSPITAL   (Japan)

^e TOHO UNIVERSITY OMORI MEDICAL CENTER   (Japan)

^f ST MARY S HOSPITAL   (Japan)

^g OSAKA NATIONAL HOSPITAL   (Japan)

^h HYOGO COLLEGE OF MEDICINE   (Japan)

ⁱ EHIME PREFECTURAL CENTRAL HOSPITAL   (Japan)

^j MIE UNIVERSITY SCHOOL OF MEDICINE   (Japan)

^k KEIO UNIVERSITY   (Japan)

^l UNIVERSITY OF OKLAHOMA COLLEGE OF MEDICINE   (United States)

more..

Author keywords

ADAMTS13 mutation; Haemolytic anaemia; Pregnancy; Thrombocytopenia; Upshaw Schulman syndrome

Indexed keywords

VON WILLEBRAND FACTOR CLEAVING PROTEINASE;

ADULT; ARTICLE; CLINICAL ARTICLE; CONTROLLED STUDY; ENZYME LINKED IMMUNOSORBENT ASSAY; FEMALE; FETUS DEATH; GENE MUTATION; GENETIC ANALYSIS; GENOTYPE; HOMOZYGOSITY; HUMAN; PREGNANCY INDUCED THROMBOCYTOPENIA; PREMATURITY; PRIORITY JOURNAL; RISK FACTOR; SINGLE NUCLEOTIDE POLYMORPHISM; THIRD TRIMESTER PREGNANCY; THROMBOCYTOPENIA; THROMBOTIC THROMBOCYTOPENIC PURPURA; TWIN PREGNANCY; UPSHAW SCHULMAN SYNDROME;

ADAM PROTEINS; ADULT; BLOTTING, WESTERN; DNA MUTATIONAL ANALYSIS; FEMALE; FETAL DEATH; GENETIC PREDISPOSITION TO DISEASE; GENOTYPE; HETEROZYGOTE; HUMANS; INFANT, NEWBORN; MALE; MUTATION; PEDIGREE; PREGNANCY; PREGNANCY COMPLICATIONS, HEMATOLOGIC; PREGNANCY TRIMESTER, SECOND; PREGNANCY TRIMESTER, THIRD; PURPURA, THROMBOTIC THROMBOCYTOPENIC; RISK;

EID: 58849165749     PISSN: 00071048     EISSN: 13652141     Source Type: Journal    
DOI: 10.1111/j.1365-2141.2008.07515.x     Document Type: Article

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