Friedreich's ataxia causes redistribution of iron, copper, and zinc in the dentate nucleus

Cerebellum

Volumn 11, Issue 4, 2012, Pages 845-860

  Koeppen, Arnulf H ^a,b   Ramirez, R Liane ^a   Yu, Devin ^a   Collins, Sarah E ^a   Qian, Jiang ^b   Parsons, Patrick J ^c,d   Yang, Karl X ^c,d   Chen, Zewu ^e   Mazurkiewicz, Joseph E ^b   Feustel, Paul J ^b  

^a STRATTON VA MEDICAL CENTER   (United States)

^b ALBANY MEDICAL COLLEGE   (United States)

^c WADSWORTH CENTER   (United States)

^d STATE UNIVERSITY OF NEW YORK   (United States)

^e X ray Optical Systems   (United States)

Author keywords

Copper; Cu; Cu++ transporting ATPase peptide (ATP7A; Dentate nucleus; Ferritin; Friedreich's ataxia; Iron; Menkes protein); Metallothionein; X ray fluorescence; Zinc; Zn superoxide dismutase

Indexed keywords

COPPER; COPPER ZINC SUPEROXIDE DISMUTASE; DIMETHYL SULFOXIDE; FERRITIN; GLIAL FIBRILLARY ACIDIC PROTEIN; GLUTAMATE DECARBOXYLASE; IRON; MACROGOL; MENKES PROTEIN; METALLOTHIONEIN I; METALLOTHIONEIN II; METALLOTHIONEIN III; NEURON SPECIFIC ENOLASE; ZINC;

ADOLESCENT; ADULT; ARTICLE; CHILD; CLINICAL ARTICLE; CONTROLLED STUDY; DENTATE NUCLEUS; FEMALE; FRIEDREICH ATAXIA; GLIOSIS; GRAY MATTER; HISTOPATHOLOGY; HUMAN; HUMAN TISSUE; IMMUNOFLUORESCENCE; IMMUNOHISTOCHEMISTRY; MALE; MICROGLIA; OLIGODENDROGLIA; PRESCHOOL CHILD; PRIORITY JOURNAL; PROTEIN LOCALIZATION; SCHOOL CHILD; WHITE MATTER; X RAY FLUORESCENCE;

ADULT; AGED; AGED, 80 AND OVER; AUTOPSY; CEREBELLAR NUCLEI; COPPER; FEMALE; FERRITINS; FRIEDREICH ATAXIA; HUMANS; IRON; MALE; MIDDLE AGED; YOUNG ADULT; ZINC;

EID: 84870447778     PISSN: 14734222     EISSN: 14734230     Source Type: Journal    
DOI: 10.1007/s12311-012-0383-5     Document Type: Article

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