Evidence for involvement of medium chain acyl-CoA dehydrogenase in the metabolism of phenylbutyrate

Molecular Genetics and Metabolism

Volumn 107, Issue 4, 2012, Pages 684-689

  Kormanik, Kaitlyn ^a,b   Kang, Heejung ^a,b   Cuebas, Dean ^c   Vockley, Jerry ^a,b   Mohsen, Al Walid ^a  

^a UNIVERSITY OF PITTSBURGH SCHOOL OF MEDICINE   (United States)

^b UNIVERSITY OF PITTSBURGH GRADUATE SCHOOL OF PUBLIC HEALTH   (United States)

^c MISSOURI STATE UNIVERSITY   (United States)

Author keywords

Buphenyl; Hyperammonemia; Medium chain acyl CoA dehydrogenase; Phenybutyrate; Urea cycle disorders

Indexed keywords

4 PHENYLBUTYRIC ACID; AMMONIA; ELECTRON TRANSFERRING FLAVOPROTEIN; MEDIUM CHAIN ACYL COENZYME A DEHYDROGENASE;

ARTICLE; CATALYSIS; DISSOCIATION CONSTANT; FATTY ACID OXIDATION; HYPERAMMONEMIA; MOLECULAR MODEL; PRIORITY JOURNAL; UREA CYCLE DISORDER;

ACYL-COA DEHYDROGENASE; CATALYTIC DOMAIN; ELECTRON-TRANSFERRING FLAVOPROTEINS; HUMANS; KINETICS; METABOLIC NETWORKS AND PATHWAYS; MOLECULAR DOCKING SIMULATION; OXIDATION-REDUCTION; PHENYLBUTYRATES; PROTEIN CONFORMATION; RECOMBINANT PROTEINS; SUBSTRATE SPECIFICITY;

EID: 84869877900     PISSN: 10967192     EISSN: 10967206     Source Type: Journal    
DOI: 10.1016/j.ymgme.2012.10.009     Document Type: Article

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