A time for reappraisal of "atypical" hemolytic uremic syndrome: Should all patients be treated the same?

European Journal of Pediatrics

Volumn 171, Issue 10, 2012, Pages 1519-1525

  Ruebner, Rebecca L ^a   Kaplan, Bernard S ^a   Copelovitch, Lawrence ^a  

^a CHILDREN S HOSPITAL OF PHILADELPHIA   (United States)

Author keywords

Acute kidney injury; Atypical hemolytic uremic syndrome; Complement proteins; Eculizumab; Microangiopathic hemolytic anemia; Nondiarrheal HUS; Thrombotic microangiopathy

Indexed keywords

COMPLEMENT COMPONENT C3; CREATININE; CYCLOPHOSPHAMIDE; ECULIZUMAB; IMMUNOGLOBULIN; METHYLPREDNISOLONE;

ADOLESCENT; ANEMIA; ARTICLE; CASE REPORT; CHILD; CONTINUOUS HEMODIAFILTRATION; CONVALESCENCE; COUGHING; DISEASE ASSOCIATION; FEMALE; FEVER; GENETIC VARIABILITY; HEMOLYTIC UREMIC SYNDROME; HUMAN; HYPERTENSION; HYPERVOLEMIA; KIDNEY BIOPSY; LIVER INJURY; MALE; MICROSCOPY; MYELITIS; OLIGURIA; PALLOR; PLASMAPHERESIS; PRESCHOOL CHILD; PRIORITY JOURNAL; THROMBOCYTOPENIA; THROMBOTIC THROMBOCYTOPENIC PURPURA; VOMITING;

ACUTE KIDNEY INJURY; ADOLESCENT; ANTIBODIES, MONOCLONAL, HUMANIZED; COMPLEMENT SYSTEM PROTEINS; DIAGNOSIS, DIFFERENTIAL; DISEASE PROGRESSION; FEMALE; HEMOLYTIC-UREMIC SYNDROME; HUMANS; INFANT; MALE; MUTATION; PHENOTYPE; PROGNOSIS; RECURRENCE;

EID: 84867578287     PISSN: 03406199     EISSN: 14321076     Source Type: Journal    
DOI: 10.1007/s00431-012-1763-z     Document Type: Article

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