Periodic fevers with aphthous stomatitis, pharyngitis, and adenitis (PFAPA)

Autoimmunity Reviews

Volumn 12, Issue 1, 2012, Pages 52-55

  Vigo, Giulia ^a   Zulian, Francesco ^a  

^a UNIVERSITY OF PADOVA   (Italy)

Author keywords

Autoinflammatory syndromes; Periodic fever; PFAPA; Tonsillectomy

Indexed keywords

BETAMETHASONE; CIMETIDINE; COLCHICINE; CXCL9 CHEMOKINE; GAMMA INTERFERON; GAMMA INTERFERON INDUCIBLE PROTEIN 10; GRANULOCYTE COLONY STIMULATING FACTOR; INTERLEUKIN 1; PREDNISONE; RECOMBINANT INTERLEUKIN 1 RECEPTOR BLOCKING AGENT; TUMOR NECROSIS FACTOR ALPHA;

ABDOMINAL PAIN; APHTHOUS STOMATITIS; ARTHRALGIA; CHILL; CLINICAL FEATURE; DIARRHEA; DIFFERENTIAL DIAGNOSIS; FAMILIAL MEDITERRANEAN FEVER; FAMILY HISTORY; FOLLOW UP; GENE EXPRESSION; HEADACHE; HUMAN; HYPERIMMUNOGLOBULINEMIA D AND PERIODIC FEVER SYNDROME; IMMUNE DYSREGULATION; INNATE IMMUNITY; ONSET AGE; PATHOGENESIS; PFAPA SYNDROME; PHARYNGITIS; RASH; REMISSION; REVIEW; SINGLE DRUG DOSE; TONSILLECTOMY; TUMOR NECROSIS FACTOR RECEPTOR ASSOCIATED PERIODIC SYNDROME;

ADRENAL CORTEX HORMONES; HEREDITARY AUTOINFLAMMATORY DISEASES; HUMANS; TONSILLECTOMY;

EID: 84866847895     PISSN: 15689972     EISSN: 18730183     Source Type: Journal    
DOI: 10.1016/j.autrev.2012.07.021     Document Type: Review

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