Two siblings with periodic fever, aphthous stomatitis, pharyngitis, adenitis (Pfapa) syndrome

Pediatric Infectious Disease Journal

Volumn 28, Issue 3, 2009, Pages 254-255

  Sampaio, Isabel Cristina Ramos Melo ^a   Rodrigo, Maria João ^a   Monteiro Marques, José Gonçalo Duque Pereira ^a  

^a HOSPITAL DE SANTA MARIA   (Portugal)

Author keywords

Marshall's syndrome; Periodic fever; PFAPA; Tonsillitis

Indexed keywords

PREDNISONE; GLUCOCORTICOID;

ADOLESCENT; ARTICLE; CASE REPORT; CHILD; CLINICAL FEATURE; DISEASE COURSE; ENVIRONMENTAL FACTOR; FEMALE; HUMAN; MALE; PFAPA SYNDROME; PRESCHOOL CHILD; PRIORITY JOURNAL; RECURRENT FEVER; SIBLING; SYNDROME DELINEATION; TONSILLITIS; APHTHOUS STOMATITIS; LYMPHADENITIS; PERIODICITY; PHARYNGITIS; PYREXIA IDIOPATHICA; SYNDROME;

CHILD; CHILD, PRESCHOOL; FEMALE; FEVER OF UNKNOWN ORIGIN; GLUCOCORTICOIDS; HUMANS; LYMPHADENITIS; MALE; PERIODICITY; PHARYNGITIS; PREDNISONE; SIBLINGS; STOMATITIS, APHTHOUS; SYNDROME;

EID: 63449118441     PISSN: 08913668     EISSN: 15320987     Source Type: Journal    
DOI: 10.1097/INF.0b013e31818c8ea5     Document Type: Article

References (6)

1. Padeh S. Periodic fever syndromes. Pediatr Clin N Am. 2005;52:577-609.
2. Tasher D, Somekh E, Dalal I. PFAPA syndrome: new clinical aspects disclosed. Arch Dis Child. 2005;91:981-984.
3. Fonseca A, Cherubini K. Clinical aspects of PFAPA syndrome (periodic fever, aphtous stomatitis, pharyngitis, and adenitis). Sci Med. 2005;15:68 -73.
4. Feder H. Periodic fever, aphtous stomatitis, pharyngitis, adenitis: a clinical review of a new syndrome. Curr Opin Pediatr. 2000;12:253-256.
5. Lierl M. Periodic fever syndromes: a diagnostic challenge for the allergist. Allergy. 2007;62:1349-1358.
6. Stojanov S, Hoffmann F, Kéry A, et al. Cytokine profile in PFAPA syndrome suggests continuous inflammation and reduced anti-inflammatory response. Eur Cytokine Netw. 2006;17:90-97.