Inner ear changes in mucopolysaccharidosis type I/Hurler syndrome

Otology and Neurotology

Volumn 33, Issue 8, 2012, Pages 1323-1327

  Kariya, Shin ^a,b   Schachern, Patricia A ^a   Nishizaki, Kazunori ^b   Paparella, Michael M ^a,c   Cureoglu, Sebahattin ^a  

^a UNIVERSITY OF MINNESOTA   (United States)

^b OKAYAMA UNIVERSITY   (Japan)

^c Paparella Ear Head and Neck Institute PA   (United States)

Author keywords

L iduronidase; Cochlea; Hearing loss; Hurler syndrome; Inner ear; Middle ear; Otitis media

Indexed keywords

ADOLESCENT; ARTICLE; CELL COUNT; CHILD; EXTERNAL EAR; FEMALE; HAIR CELL; HUMAN; HURLER SYNDROME; INFANT; INNER EAR; MALE; MESODERM; PATHOLOGY; PRESCHOOL CHILD; SPIRAL GANGLION; SPIRAL LIGAMENT; STRIA VASCULARIS; TEMPORAL BONE;

ADOLESCENT; CELL COUNT; CHILD; CHILD, PRESCHOOL; EAR, EXTERNAL; EAR, INNER; FEMALE; HAIR CELLS, VESTIBULAR; HUMANS; INFANT; MALE; MESODERM; MUCOPOLYSACCHARIDOSIS I; SPIRAL GANGLION; SPIRAL LIGAMENT OF COCHLEA; STRIA VASCULARIS; TEMPORAL BONE;

EID: 84866611512     PISSN: 15317129     EISSN: 15374505     Source Type: Journal    
DOI: 10.1097/MAO.0b013e3182659cc3     Document Type: Article

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