Tissue-Specific Strategies of the Very-Long Chain Acyl-CoA Dehydrogenase-Deficient (VLCAD-/-) Mouse to Compensate a Defective Fatty Acid β-Oxidation

PLoS ONE

Volumn 7, Issue 9, 2012, Pages

  Tucci, Sara ^a   Herebian, Diran ^a   Sturm, Marga ^a   Seibt, Annette ^a   Spiekerkoetter, Ute ^a  

^a UNIVERSITY HOSPITAL DÜSSELDORF   (Germany)

Author keywords

[No Author keywords available]

Indexed keywords

CARBON; FATTY ACID; LONG CHAIN ACYL COENZYME A DEHYDROGENASE; LONG CHAIN TRIACYLGLYCEROL; MEDIUM CHAIN ACYL COENZYME A DEHYDROGENASE; MEDIUM CHAIN TRIACYLGLYCEROL; MESSENGER RNA; UNCLASSIFIED DRUG; VERY LONG CHAIN ACYL COENZYME A DEHYDROGENASE;

ADAPTATION; AMINO ACID SEQUENCE; ANATOMICAL VARIATION; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CONTROLLED STUDY; DIET SUPPLEMENTATION; ENZYME ACTIVITY; ENZYME DEFICIENCY; ENZYME SUBSTRATE; FATTY ACID OXIDATION; GASTROCNEMIUS MUSCLE; GLYCOLYSIS; HEART; LIVER; MOUSE; NONHUMAN; NUCLEOTIDE SEQUENCE; NUTRITIONAL ASSESSMENT; PROTEIN ANALYSIS; PROTEIN EXPRESSION; PROTEIN FUNCTION; SKELETAL MUSCLE;

ACYL-COA DEHYDROGENASE, LONG-CHAIN; ACYL-COA DEHYDROGENASES; ADAPTATION, PHYSIOLOGICAL; ANIMALS; CITRATE (SI)-SYNTHASE; DIET; DISEASE MODELS, ANIMAL; FATTY ACIDS; HOMOZYGOTE; LIPID METABOLISM, INBORN ERRORS; LIVER; MICE; MICE, KNOCKOUT; MITOCHONDRIAL DISEASES; MUSCLE, SKELETAL; MUSCULAR DISEASES; MYOCARDIUM; ORGAN SPECIFICITY; OXIDATION-REDUCTION; PHENOTYPE; RNA, MESSENGER;

MUS;

EID: 84866378534     PISSN: None     EISSN: 19326203     Source Type: Journal    
DOI: 10.1371/journal.pone.0045429     Document Type: Article

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