Familial Hemophagocytic Lymphohistiocytosis May Present during Adulthood: Clinical and Genetic Features of a Small Series

PLoS ONE

Volumn 7, Issue 9, 2012, Pages

  Sieni, Elena ^a   Cetica, Valentina ^a   Piccin, Andrea ^b   Gherlinzoni, Filippo ^c   Sasso, Ferdinando Carlo ^d   Rabusin, Marco ^e   Attard, Luciano ^f   Bosi, Alberto ^g   Pende, Daniela ^h   Moretta, Lorenzo ⁱ   Aricò, Maurizio ^a  

^a UNIVERSITY OF FLORENCE   (Italy)

^b San Maurizio Regional Hospital   (Italy)

^c OSPEDALE CA FONCELLO   (Italy)

^d SECOND UNIVERSITY OF NAPLES   (Italy)

^e INSTITUTE FOR MATERNAL AND CHILD HEALTH IRCCS BURLO GAROFOLO   (Italy)

^f UNIVERSITY OF BOLOGNA   (Italy)

^g CAREGGI UNIVERSITY HOSPITAL   (Italy)

^h UNIVERSITY OF GENOA   (Italy)

ⁱ G GASLINI INSTITUTE   (Italy)

Author keywords

[No Author keywords available]

Indexed keywords

GLUCOCORTICOID; PREDNISONE;

ADULT; ARTICLE; CENTRAL NERVOUS SYSTEM DISEASE; CLINICAL ARTICLE; CLINICAL FEATURE; CYTOPENIA; DIFFERENTIAL DIAGNOSIS; DISEASE CONTROL; DRUG DOSE REDUCTION; DRUG MEGADOSE; FEMALE; FLOW CYTOMETRY; GENETIC ANALYSIS; GENETIC DISORDER; HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS; HUMAN; LIVER DISEASE; LOW DRUG DOSE; MALE; RETROSPECTIVE STUDY; STEM CELL TRANSPLANTATION;

ADOLESCENT; ADULT; AGE OF ONSET; FEMALE; HUMANS; LYMPHOHISTIOCYTOSIS, HEMOPHAGOCYTIC; MALE;

EID: 84866087810     PISSN: None     EISSN: 19326203     Source Type: Journal    
DOI: 10.1371/journal.pone.0044649     Document Type: Article

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