Survival, but not maturation, is affected in neutrophil progenitors from GSD-1b patients

Journal of Inherited Metabolic Disease

Volumn 35, Issue 2, 2012, Pages 287-300

  Visser, Gepke ^a   De Jager, Wilco ^b   Verhagen, Liesbeth P ^b   Smit, G Peter A ^c   Wijburg, Frits A ^d   Prakken, Berent J ^b   Coffer, Paul J ^a,b   Buitenhuis, Miranda ^e  

^a UNIVERSITY MEDICAL CENTER UTRECHT   (Netherlands)

^b UNIVERSITY MEDICAL CENTER UTRECHT   (Netherlands)

^c UNIVERSITY OF GRONINGEN   (Netherlands)

^d ACADEMIC MEDICAL CENTER   (Netherlands)

^e ERASMUS MEDICAL CENTER   (Netherlands)

Author keywords

[No Author keywords available]

Indexed keywords

CD34 ANTIGEN; COMPLEMENT COMPONENT C3B RECEPTOR; GAMMA INTERFERON; GLUCOSE; GRANULOCYTE COLONY STIMULATING FACTOR; INTERLEUKIN 1ALPHA; INTERLEUKIN 1BETA; INTERLEUKIN 6; INTERLEUKIN 8; MACROPHAGE INFLAMMATORY PROTEIN 1ALPHA; MACROPHAGE INFLAMMATORY PROTEIN 3BETA; MONOCYTE CHEMOTACTIC PROTEIN 1; STROMAL CELL DERIVED FACTOR 1;

ADOLESCENT; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; APOPTOSIS; ARTICLE; BONE MARROW CELL; CELL DIFFERENTIATION; CELL MATURATION; CELL SURVIVAL; CHILD; CLINICAL ARTICLE; CONTROLLED STUDY; CYTOKINE PRODUCTION; DISEASE ASSOCIATION; DOWN REGULATION; ENTERITIS; EX VIVO STUDY; FEMALE; GLYCOGEN STORAGE DISEASE TYPE 1; GLYCOGEN STORAGE DISEASE TYPE 1B; HEMATOPOIETIC STEM CELL; HUMAN; HUMAN CELL; HUMAN TISSUE; IN VITRO STUDY; IN VIVO STUDY; MALE; MESENCHYMAL STROMA CELL; MOUSE; NEUTROPENIA; NEUTROPHIL CHEMOTAXIS; NEUTROPHIL COUNT; NONHUMAN; PRESCHOOL CHILD; PROTEIN EXPRESSION; UPREGULATION;

ADOLESCENT; ANIMALS; ANTIPORTERS; APOPTOSIS; CELL DIFFERENTIATION; CHILD; CHILD, PRESCHOOL; CYTOKINES; FEMALE; GLUCOSE; GLYCOGEN STORAGE DISEASE TYPE I; HEMATOPOIETIC STEM CELLS; HOMEOSTASIS; HUMANS; INFLAMMATORY BOWEL DISEASES; INTESTINES; LEUKOCYTES, MONONUCLEAR; MALE; MESENCHYMAL STROMAL CELLS; MICE; MICE, INBRED NOD; MICE, SCID; MONOSACCHARIDE TRANSPORT PROTEINS; NEUTROPENIA; NEUTROPHILS; SURVIVAL RATE;

EID: 84863438062     PISSN: 01418955     EISSN: 15732665     Source Type: Journal    
DOI: 10.1007/s10545-011-9379-4     Document Type: Article

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