Abnormal gangliosides are localized in lipid rafts in Sanfilippo (MPS3a) mouse brain

Neurochemical Research

Volumn 37, Issue 6, 2012, Pages 1372-1380

  Dawson, G ^a   Fuller, M ^b   Helmsley, K M ^b   Hopwood, J J ^b  

^a UNIVERSITY OF CHICAGO   (United States)

^b Lysosomal Diseases Research Unit   (Australia)

Author keywords

Bis(monoacylglycerol) phosphate; Gangliosides; Lipid rafts; Mass spectrometry; Mouse brain; Sanfilippo

Indexed keywords

CERAMIDE; FATTY ACID; GALACTOSYLCERAMIDE; GANGLIOSIDE; GANGLIOSIDE GM2; GANGLIOSIDE GM3; HEPARAN SULFATE; LYSOBISPHOSPHATIDIC ACID; MONOACYLGLYCEROL; OLIGOSACCHARIDE; PHOSPHATE; PHOSPHATIDYLGLYCEROL; SPHINGOMYELIN; UNCLASSIFIED DRUG;

ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; BIOACCUMULATION; CONTROLLED STUDY; ENDOSOME; HEMISPHERE; HIGH PERFORMANCE LIQUID CHROMATOGRAPHY; LIPID ANALYSIS; LIPID RAFT; LIPIDOSIS; LYSOSOME; MASS SPECTROMETRY; MOUSE; NERVE CELL; NONHUMAN; PRIORITY JOURNAL; SANFILIPPO SYNDROME;

ANIMALS; BRAIN; G(M2) GANGLIOSIDE; G(M3) GANGLIOSIDE; GANGLIOSIDES; LYSOPHOSPHOLIPIDS; LYSOSOMES; MEMBRANE MICRODOMAINS; MICE; MONOGLYCERIDES; MUCOPOLYSACCHARIDOSIS III; TANDEM MASS SPECTROMETRY;

EID: 84862886325     PISSN: 03643190     EISSN: 15736903     Source Type: Journal    
DOI: 10.1007/s11064-012-0761-x     Document Type: Article

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