-
1
-
-
79957946294
-
Managing cystic fibrosis: Strategies that increase life expectancy and improve quality of life
-
Cohen-Cymberknoh M, Shoseyov D, Kerem E. Managing cystic fibrosis: strategies that increase life expectancy and improve quality of life. Am J Respir Crit Care Med 2011;183:1463-1471.
-
(2011)
Am J Respir Crit Care Med
, vol.183
, pp. 1463-1471
-
-
Cohen-Cymberknoh, M.1
Shoseyov, D.2
Kerem, E.3
-
2
-
-
77950914953
-
Treatment of early Pseudomonas aeruginosa infection in patients with cystic fibrosis: The ELITE trial
-
ELITE Study Group
-
Ratjen F, Munck A, Kho P, Angyalosi G; ELITE Study Group. Treatment of early Pseudomonas aeruginosa infection in patients with cystic fibrosis: the ELITE trial. Thorax 2010;65:286-291.
-
(2010)
Thorax
, vol.65
, pp. 286-291
-
-
Ratjen, F.1
Munck, A.2
Kho, P.3
Angyalosi, G.4
-
3
-
-
80052511405
-
Comparative efficacy and safety of 4 randomized regimens to treat early Pseudomonas aeruginosa infection in children with cystic fibrosis
-
Early Pseudomonas Infection Control (EPIC) Investigators
-
Treggiari MM, Retsch-Bogart G, Mayer-Hamblett N, Khan U, Kulich M, Kronmal R, Williams J, Hiatt P, Gibson RL, Spencer T, et al.; Early Pseudomonas Infection Control (EPIC) Investigators. Comparative efficacy and safety of 4 randomized regimens to treat early Pseudomonas aeruginosa infection in children with cystic fibrosis. Arch Pediatr Adolesc Med 2011;165:847-856.
-
(2011)
Arch Pediatr Adolesc Med
, vol.165
, pp. 847-856
-
-
Treggiari, M.M.1
Retsch-Bogart, G.2
Mayer-Hamblett, N.3
Khan, U.4
Kulich, M.5
Kronmal, R.6
Williams, J.7
Hiatt, P.8
Gibson, R.L.9
Spencer, T.10
-
4
-
-
0032718969
-
Diagnostic accuracy of oropharyngeal cultures in infants and young children with cystic fibrosis
-
DOI 10.1002/(SICI)1099-0496(199911)28:5<321::AID-PPUL3>3.0.CO;2-V
-
Rosenfeld M, Emerson J, Accurso F, Armstrong D, Castile R, Grimwood K, Hiatt P, McCoy K, McNamara S, Ramsey B, et al. Diagnostic accuracy of oropharyngeal cultures in infants and young children with cystic fibrosis. Pediatr Pulmonol 1999;28:321-328. (Pubitemid 29523443)
-
(1999)
Pediatric Pulmonology
, vol.28
, Issue.5
, pp. 321-328
-
-
Rosenfeld, M.1
Emerson, J.2
Accurso, F.3
Armstrong, D.4
Castile, R.5
Grimwood, K.6
Hiatt, P.7
McCoy, K.8
McNamara, S.9
Ramsey, B.10
Wagener, J.11
-
5
-
-
79960151730
-
Effect of bronchoalveolar lavage-directed therapy on Pseudomonas aeruginosa infection and structural lung injury in children with cystic fibrosis: A randomized trial
-
ACFBAL Study Investigators
-
Wainwright CE, Vidmar S, Armstrong DS, Byrnes CA, Carlin JB, Cheney J, Cooper PJ, Grimwood K, Moodie M, Robertson CF, et al.; ACFBAL Study Investigators. Effect of bronchoalveolar lavage-directed therapy on Pseudomonas aeruginosa infection and structural lung injury in children with cystic fibrosis: a randomized trial. JAMA 2011;306:163-171.
-
(2011)
JAMA
, vol.306
, pp. 163-171
-
-
Wainwright, C.E.1
Vidmar, S.2
Armstrong, D.S.3
Byrnes, C.A.4
Carlin, J.B.5
Cheney, J.6
Cooper, P.J.7
Grimwood, K.8
Moodie, M.9
Robertson, C.F.10
-
6
-
-
80051561535
-
Pseudomonas aeruginosa population diversity and turnover in cystic fibrosis chronic infections
-
Mowat E, Paterson S, Fothergill JL, Wright EA, Ledson MJ, Walshaw MJ, Brockhurst MA, Winstanley C. Pseudomonas aeruginosa population diversity and turnover in cystic fibrosis chronic infections. Am J Respir Crit Care Med 2011;183:1674-1679.
-
(2011)
Am J Respir Crit Care Med
, vol.183
, pp. 1674-1679
-
-
Mowat, E.1
Paterson, S.2
Fothergill, J.L.3
Wright, E.A.4
Ledson, M.J.5
Walshaw, M.J.6
Brockhurst, M.A.7
Winstanley, C.8
-
7
-
-
80051571499
-
Complex pseudomonas population structure in cystic fibrosis airway infections
-
Workentine M, Surrette MG. Complex pseudomonas population structure in cystic fibrosis airway infections. Am J Respir Crit Care Med 2011;183:1581-1583.
-
(2011)
Am J Respir Crit Care Med
, vol.183
, pp. 1581-1583
-
-
Workentine, M.1
Surrette, M.G.2
-
8
-
-
78751559949
-
Clinical significance of microbacterial infection and adaptation in cystic fibrosis
-
Hauser AR, Jain M, Bar-Meir M, McColley SA. Clinical significance of microbacterial infection and adaptation in cystic fibrosis. Clin Microbiol Rev 2011;24:29-70.
-
(2011)
Clin Microbiol Rev
, vol.24
, pp. 29-70
-
-
Hauser, A.R.1
Jain, M.2
Bar-Meir, M.3
McColley, S.A.4
-
9
-
-
78751515589
-
Stenotrophomonas maltophilia in cystic fibrosis: Serologic response and effect on lung disease
-
Waters V, Yau Y, Prasad S, Lu A, Atenafu E, Crandall I, Tom S, Tullis E, Ratjen F. Stenotrophomonas maltophilia in cystic fibrosis: serologic response and effect on lung disease. Am J Respir Crit Care Med 2011;183:635-640.
-
(2011)
Am J Respir Crit Care Med
, vol.183
, pp. 635-640
-
-
Waters, V.1
Yau, Y.2
Prasad, S.3
Lu, A.4
Atenafu, E.5
Crandall, I.6
Tom, S.7
Tullis, E.8
Ratjen, F.9
-
10
-
-
79952205053
-
Stenotrophomonas maltophilia in cystic fibrosis: Guilty or innocent?
-
Colin AA, Rabin HR. Stenotrophomonas maltophilia in cystic fibrosis: guilty or innocent? Am J Respir Crit Care Med 2011;183:564-566.
-
(2011)
Am J Respir Crit Care Med
, vol.183
, pp. 564-566
-
-
Colin, A.A.1
Rabin, H.R.2
-
11
-
-
0026831341
-
Mucoid Pseudomonas aeruginosa is a marker of poor survival in cystic fibrosis
-
Henry RL, Mellis CM, Petrovic L. Mucoid Pseudomonas aeruginosa is a marker of poor survival in cystic fibrosis. Pediatr Pulmonol 1992;12:158-161.
-
(1992)
Pediatr Pulmonol
, vol.12
, pp. 158-161
-
-
Henry, R.L.1
Mellis, C.M.2
Petrovic, L.3
-
12
-
-
78650799199
-
Mucoid and nonmucoid Burkolderia cepacia complex bacteria in cystic fibrosis infections
-
Zlosnik JEA, Costa PS, Brant R, Mori PYB, Hird TJ, Fraenkel MC, Wilcox PG, Davidson GAF, Speert DP. Mucoid and nonmucoid Burkolderia cepacia complex bacteria in cystic fibrosis infections. Am J Respir Crit Care Med 2011;183:67-72.
-
(2011)
Am J Respir Crit Care Med
, vol.183
, pp. 67-72
-
-
Zlosnik, J.E.A.1
Costa, P.S.2
Brant, R.3
Mori, P.Y.B.4
Hird, T.J.5
Fraenkel, M.C.6
Wilcox, P.G.7
Davidson, G.A.F.8
Speert, D.P.9
-
13
-
-
33745761197
-
Inhaled L-arginine improves exhaled nitric oxide and pulmonary function in patients with cystic fibrosis
-
DOI 10.1164/rccm.200509-1439OC
-
Grasemann H, Kurtz F, Ratjen F. Inhaled L-arginine improves exhaled nitric oxide and pulmonary function in patients with cystic fibrosis. Am J Respir Crit Care Med 2006;174:208-212. (Pubitemid 44015394)
-
(2006)
American Journal of Respiratory and Critical Care Medicine
, vol.174
, Issue.2
, pp. 208-212
-
-
Grasemann, H.1
Kurtz, F.2
Ratjen, F.3
-
14
-
-
30444439420
-
Increased arginase activity in cystic fibrosis airways
-
DOI 10.1164/rccm.200502-253OC
-
Grasemann H, Schwiertz R, Matthiesen S, Racke K, Ratjen F. Increased arginase activity in cystic fibrosis airways. Am J Respir Crit Care Med 2005;172:1523-1528. (Pubitemid 43076540)
-
(2005)
American Journal of Respiratory and Critical Care Medicine
, vol.172
, Issue.12
, pp. 1523-1528
-
-
Grasemann, H.1
Schwiertz, R.2
Matthiesen, S.3
Racke, K.4
Ratjen, F.5
-
15
-
-
79956227191
-
Asymmetric dimethylarginine contributes to airway nitric oxide deficiency in patients with cystic fibrosis
-
Grasemann H, Al-Saleh S, Scott JA, Shehnaz D, Mehl A, Amin R, Rafii M, Pencharz P, Belik J, Ratjen F. Asymmetric dimethylarginine contributes to airway nitric oxide deficiency in patients with cystic fibrosis. Am J Respir Crit Care Med 2011;183:1363-1368.
-
(2011)
Am J Respir Crit Care Med
, vol.183
, pp. 1363-1368
-
-
Grasemann, H.1
Al-Saleh, S.2
Scott, J.A.3
Shehnaz, D.4
Mehl, A.5
Amin, R.6
Rafii, M.7
Pencharz, P.8
Belik, J.9
Ratjen, F.10
-
16
-
-
79956215422
-
Nitrogen balance in the ecosystem of the cystic fibrosis lung
-
Marozkina NV, Gaston B. Nitrogen balance in the ecosystem of the cystic fibrosis lung. Am J Respir Crit Care Med 2011;183:1290-1293.
-
(2011)
Am J Respir Crit Care Med
, vol.183
, pp. 1290-1293
-
-
Marozkina, N.V.1
Gaston, B.2
-
17
-
-
80051572617
-
Infection, inflammation, and lung function decline in infants with cystic fibrosis
-
Australian Respiratory Early Surveillance Team for Cystic Fibrosis (AREST CF)
-
Pillarisetti N, Williamson E, Linnane B, Skoric B, Robertson CF, Robinson P, Massie J, Hall GL, Sly P, Stick S, et al.; Australian Respiratory Early Surveillance Team for Cystic Fibrosis (AREST CF). Infection, inflammation, and lung function decline in infants with cystic fibrosis. Am J Respir Crit Care Med 2011;184:75-81.
-
(2011)
Am J Respir Crit Care Med
, vol.184
, pp. 75-81
-
-
Pillarisetti, N.1
Williamson, E.2
Linnane, B.3
Skoric, B.4
Robertson, C.F.5
Robinson, P.6
Massie, J.7
Hall, G.L.8
Sly, P.9
Stick, S.10
-
18
-
-
80051553123
-
The th17 pathway in cystic fibrosis lung disease
-
Tan H, Regamey N, Brown S, Bush A, Lloyd CM, Davies JC. The th17 pathway in cystic fibrosis lung disease. Am J Respir Crit CareMed 2011; 184:252-258.
-
(2011)
Am J Respir Crit CareMed
, vol.184
, pp. 252-258
-
-
Tan, H.1
Regamey, N.2
Brown, S.3
Bush, A.4
Lloyd, C.M.5
Davies, J.C.6
-
19
-
-
80051565623
-
IL-17 in cystic fibrosis: More than just th17 cells
-
Dubin PJ, Tolls JK. IL-17 in cystic fibrosis: more than just th17 cells. Am J Respir Crit Care Med 2011;184:155-157.
-
(2011)
Am J Respir Crit Care Med
, vol.184
, pp. 155-157
-
-
Dubin, P.J.1
Tolls, J.K.2
-
20
-
-
79957957677
-
Nebulized hypertonic saline decreases IL-8 in sputum of patients with cystic fibrosis
-
Reeves EP, Williamson M, O'Neill SJ, Greally P, McElvaney NG. Nebulized hypertonic saline decreases IL-8 in sputum of patients with cystic fibrosis. Am J Respir Crit Care Med 2011;183:1517-1523.
-
(2011)
Am J Respir Crit Care Med
, vol.183
, pp. 1517-1523
-
-
Reeves, E.P.1
Williamson, M.2
O'Neill, S.J.3
Greally, P.4
McElvaney, N.G.5
-
22
-
-
36248953255
-
Cystic fibrosis pulmonary guidelines: Chronic medications for maintenance of lung health
-
Flume PA, O'Sullivan BP, Robinson KA, Goss CH, Mogayzel PJ Jr, Willey-Courand DB, Bujan J, Finder J, Lester M, Quittell L, et al. Cystic fibrosis pulmonary guidelines: chronic medications for maintenance of lung health. Am J Respir Crit Care Med 2001;176:957-969.
-
(2001)
Am J Respir Crit Care Med
, vol.176
, pp. 957-969
-
-
Flume, P.A.1
O'Sullivan, B.P.2
Robinson, K.A.3
Goss, C.H.4
Mogayzel Jr., P.J.5
Willey-Courand, D.B.6
Bujan, J.7
Finder, J.8
Lester, M.9
Quittell, L.10
-
23
-
-
79957942626
-
Levofloxacin inhalation solution (MP-376) in patients with cystic fibrosis with Pseudomonas aeruginosa
-
Mpex 204 Study Group
-
Geller DE, Flume PA, Staab D, Fischer R, Loutit JS. Conrad DJ; Mpex 204 Study Group. Levofloxacin inhalation solution (MP-376) in patients with cystic fibrosis with Pseudomonas aeruginosa. Am J Respir Crit Care Med 2011;183:1510-1516.
-
(2011)
Am J Respir Crit Care Med
, vol.183
, pp. 1510-1516
-
-
Geller, D.E.1
Flume, P.A.2
Staab, D.3
Fischer, R.4
Loutit, J.S.5
Conrad, D.J.6
-
24
-
-
34547949974
-
Phase 2 randomized safety and efficacy trial of nebulized denufosol tetrasodium in cystic fibrosis
-
DOI 10.1164/rccm.200608-1238OC
-
Deterding RR, Lavange LM, Engels JM, Mathews DW, Coquillette SJ, Brody AS, Millard SP, Ramsey BW. Phase II randomized safety and efficacy trial of denufosol tetrasodium in cystic fibrosis. Am J Respir Crit Care Med 2007;17:362-369. (Pubitemid 47267470)
-
(2007)
American Journal of Respiratory and Critical Care Medicine
, vol.176
, Issue.4
, pp. 362-369
-
-
Deterding, R.R.1
LaVange, L.M.2
Engels, J.M.3
Mathews, D.W.4
Coquillette, S.J.5
Brody, A.S.6
Millard, S.P.7
Ramsey, B.W.8
-
25
-
-
79952211206
-
Denufosol tetrasodium in patients with cystic fibrosis and normal to mildly impaired lung function
-
TIGER-1 Investigator Study Group
-
Accurso FJ, Moss RB, Wilmott RW, Anbar RD, Schaberg AE, Durham TA. Ramsey BW; TIGER-1 Investigator Study Group. Denufosol tetrasodium in patients with cystic fibrosis and normal to mildly impaired lung function. Am J Respir Crit Care Med 2011;183:627-634.
-
(2011)
Am J Respir Crit Care Med
, vol.183
, pp. 627-634
-
-
Accurso, F.J.1
Moss, R.B.2
Wilmott, R.W.3
Anbar, R.D.4
Schaberg, A.E.5
Durham, T.A.6
Ramsey, B.W.7
-
26
-
-
80051566309
-
Exciting new clinical trials in cystic fibrosis: Infants need not apply
-
Stick SM, Sly PD. Exciting new clinical trials in cystic fibrosis: infants need not apply. Am J Respir Crit Care Med 2011;183:1577-1578.
-
(2011)
Am J Respir Crit Care Med
, vol.183
, pp. 1577-1578
-
-
Stick, S.M.1
Sly, P.D.2
-
27
-
-
80455162465
-
A CFTR potentiator in patients with cystic fibrosis and the G551D mutation
-
Ramsey BW, Davies J, McElvaney NG, Tullis E, Bell SC, Drevinek P, Griese M, McKone EF, Wainwright CE, Konstan MW, et al. A CFTR potentiator in patients with cystic fibrosis and the G551D mutation. N Engl J Med 2011;365:1663-1672.
-
(2011)
N Engl J Med
, vol.365
, pp. 1663-1672
-
-
Ramsey, B.W.1
Davies, J.2
McElvaney, N.G.3
Tullis, E.4
Bell, S.C.5
Drevinek, P.6
Griese, M.7
McKone, E.F.8
Wainwright, C.E.9
Konstan, M.W.10
-
28
-
-
80053402077
-
Chest computed tomography scores of severity are associated with future lung disease progression in children with cystic fibrosis
-
Sanders DB, Li Z, Brody AS, Farrell PM. Chest computed tomography scores of severity are associated with future lung disease progression in children with cystic fibrosis. Am J Respir Crit Care Med 2011;184:816-821.
-
(2011)
Am J Respir Crit Care Med
, vol.184
, pp. 816-821
-
-
Sanders, D.B.1
Li, Z.2
Brody, A.S.3
Farrell, P.M.4
-
29
-
-
79952504576
-
Lung clearance index at 4 years predicts subsequent lung function in children with cystic fibrosis
-
The London Cystic Fibrosis Collaboration
-
Aurora P, Stanojevic S, Wade A, Oliver C, Kozlowska W, Lum S, Bush A, Price J, Carr SB, Shankar A, et al.; The London Cystic Fibrosis Collaboration. Lung clearance index at 4 years predicts subsequent lung function in children with cystic fibrosis. Am J Respir Crit Care Med 2011;183:752-758.
-
(2011)
Am J Respir Crit Care Med
, vol.183
, pp. 752-758
-
-
Aurora, P.1
Stanojevic, S.2
Wade, A.3
Oliver, C.4
Kozlowska, W.5
Lum, S.6
Bush, A.7
Price, J.8
Carr, S.B.9
Shankar, A.10
-
30
-
-
80053411033
-
The importance of imaging in cystic fibrosis
-
Daines C, Morgan W. The importance of imaging in cystic fibrosis. Am J Respir Crit Care Med 2011;184:751-752.
-
(2011)
Am J Respir Crit Care Med
, vol.184
, pp. 751-752
-
-
Daines, C.1
Morgan, W.2
-
31
-
-
81455138216
-
Risk factors for chronic kidney disease in adults with cystic fibrosis
-
Quon BS, Mayer-Hamblett N, Aitken ML, Smyth AR, Goss CH. Risk factors for chronic kidney disease in adults with cystic fibrosis. Am J Respir Crit Care Med 2011;184:1147-1152.
-
(2011)
Am J Respir Crit Care Med
, vol.184
, pp. 1147-1152
-
-
Quon, B.S.1
Mayer-Hamblett, N.2
Aitken, M.L.3
Smyth, A.R.4
Goss, C.H.5
-
32
-
-
81455128877
-
Chronic kidney disease: A new morbidity of cystic fibrosis or an old morbidity of diabetes mellitus?
-
Schechter MS, Stecenko AA. Chronic kidney disease: a new morbidity of cystic fibrosis or an old morbidity of diabetes mellitus? Am J Respir Crit Care Med 2011;184:1101-1102.
-
(2011)
Am J Respir Crit Care Med
, vol.184
, pp. 1101-1102
-
-
Schechter, M.S.1
Stecenko, A.A.2
|